Extramedullary Hematopoiesis of the Sphenoid Sinus Associated with Hereditary Spherocytosis: A Case Report

Extramedullary hematopoiesis is a rare cause of a sinonasal mass that presents unique diagnostic and treatment challenges. While there are numerous reports of patients with hereditary spherocytosis developing extramedullary hematopoiesis in the posterior mediastinum, involvement in the paranasal sinuses has not previously been described. Here, we present the first case of a patient with hereditary spherocytosis developing extramedullary hematopoiesis in the sphenoid sinus.

Source: International Journal of Pediatric Otorhinolaryngology - August 10, 2018 Category: ENT & OMF Authors: Jaron Densky, Tirth Patel, Ashleigh Halderman, Prashant Malhotra Tags: Case Report Source Type: research