P258 Missed sequelae of CVID: a case presentation

While CVID is the most common form of clinically significant primary immunodeficiency, due to its heterogeneous features and complications, there continues to be a 5 year diagnostic delay. In patients with CVID, there is a 2-8% lifetime risk of lymphoma and about 10% develop granulomatous disease. Longer diagnostic delays, presence of malignancy, and granulomatous/lymphocytic interstitial lung disease (GLILD) are associated with increased risk of death. This 59 year old female, misdiagnosed with sarcoidosis, was found to have CVID-related GLILD and lymphoma.
Source: Annals of Allergy, Asthma and Immunology - Category: Allergy & Immunology Authors: Source Type: research