Arthrogryposis multiplex congenita causing hypercapnic respiratory failure and airway obstruction in an adult patient

This case highlights arthrogryposis multiplex congenita (AMC) as a rare cause of hypercapnoeic respiratory failure and airway obstruction in adults and emphasizes the usage of leak-port in tracheostomy-NIV (non-invasive-ventilation) specially in resource poor setting when the tracheostomy-NIV mask is unavailable. Key messageThis case highlights arthrogryposis multiplex congenita (AMC) as a rare cause of hypercapnoeic respiratory failure and airway obstruction in adults and emphasizes the usage of leak-port in tracheostomy-NIV (non-invasive-ventilation) specially in resource poor setting when the tracheostomy-NIV mask is unavailable.

Source: Respirology Case Reports - April 24, 2024 Category: Respiratory Medicine Authors: Harshana Bandara, Sathiaruban Sathiyamoorthy, Dinusha Withana, Tharindi Dissanayake, Harshani Athapaththu, Wathsala Gunasinghe Tags: CLINICAL IMAGE Source Type: research