Adult ocular adnexal xanthogranulomatous disease associated with immunoglobulin G4-related disease: an unusual association

Reumatismo. 2024 Mar 22;76(1). doi: 10.4081/reumatismo.2024.1641.ABSTRACTAdult-onset xanthogranuloma (AOX) and immunoglobulin G4-related disease (IgG4-RD) are uncommon fibrosing conditions that may exhibit localized ocular manifestations and occasionally systemic symptoms. These conditions exhibit overlapping clinical and histological features, suggesting a potential correlation between them, although their exact relationship remains unclear. This paper presents the case of a black male patient exhibiting typical histological indications of both AOX and IgG4-RD. The patient responded positively to corticosteroid treatment.PMID:38523581 | DOI:10.4081/reumatismo.2024.1641

Source: Reumatismo - March 25, 2024 Category: Rheumatology Authors: A R De Santana M D L Castro de Oliveira Figueir ôa A L Souza Pedreira G L Behrens Pinto M B Santiago Source Type: research