Measuring the burden of cystic fibrosis: A scoping review

Cystic fibrosis (CF) is a rare autosomal recessive disease that affects multiple organ systems, including the respiratory, digestive and reproductive systems [1]. The implementation of multidisciplinary care teams, newborn screening and advances in supportive medicines has led to steady improvement in CF health outcomes over the past five decades [2]. Nonetheless, in 2019 in North America, Europe and the UK the median age of survival was in the 40 ′s and 50′s [3–5].

Source: Journal of Cystic Fibrosis - December 2, 2023 Category: Respiratory Medicine Authors: Zain M. Cheema, Lilian C. Gomez, Noah Johnson, Olivier D. Laflamme, Harvey R. Rabin, Kim Steele, Jeanette Leong, Stephanie Y. Cheng, Bradley S. Quon, Anne L. Stephenson, W. Dominika Wranik, Mohsen Sadatsafavi, Sanja Stanojevic Tags: Original Article Source Type: research