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Predictors of mortality and cardiovascular outcomes in Emery-Dreifuss Muscular Dystrophy in a long-term follow-up
CONCLUSIONS: LMNA mutation and higher NT-proBNP concentration were associated with increased mortality in EDMD. Lower TAPSE was a predictor of a composite secondary endpoint in EDMD.PMID:34783354 | DOI:10.33963/KP.a2021.0159
Source: Kardiologia Polska - November 16, 2021 Category: Cardiology Authors: Micha ł Marchel Agnieszka Madej-Pilarczyk Roman Steckiewicz Przemys ław Stolarz Micha ł Peller Agata Tymi ńska Ewa Ostrowska Krzysztof Oziera ński Pawe ł Balsam Marcin Grabowski Grzegorz Opolski Source Type: research