112 The lung clearance index to inform clinical decision-making in early cystic fibrosis lung disease: findings from a prospective study
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: L. Perrem, S. Jeanneret-Manning, S. Stanojevic, D. Stephanie, T. Edwards, M. Rosenfeld, F. Ratjen Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
113 Effect of discontinuing hypertonic saline or dornase alfa on mucociliary clearance in people with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: The SIMPLIFY-MCC Study
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: S. Donaldson, T. Corcoran, J. Pilewski, B. Laube, P. Mogayzel, A. Ceppe, J. Wu, K. Zeman, S. Rowe, D. Nichols, A. Gifford, W. Bennett, N. Hamblett Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
114 Lung T1-MRI and multiple breath washout detect longitudinal lung changes in children beginning elexacaftor-tezacaftor-ivacaftor therapy
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: S. Nasr, C. MacAskill, M. Kretzler, B. Bella, S. Farr, K. McBennett, C. Ren, C. Flask Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
115 Baseline symptom tracking in the Home Reported Outcome Study (HERO-2) in people with cystic fibrosis taking elexacaftor-tezacaftorivacaftor
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: B. Rosen, K. Psoter, K. Sabadosa, G. Hergenroeder, L. Bendy, N. Luo, C. Zhang, C. Ren, C. Brown Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
116 First-in-human clinical trial with SPL84, an antisense oligonucleotide for treatment of people with cystic fibrosis with the 3849 +10 Kb C - > T mutation
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: Y. Caraco, M. Wanounou, L. Friedman, A. Cohen, G. Hart, E. Kerem Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
117 Maternal and fetal outcomes in the era of CFTR modulators (MAYFLOWERS) study: interim results
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: R. Jain, I. Emerman, P. Vu, N. Cameron, A. Keller, A. Wilson, M. Putman, J. Taylor-Cousar Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
118 Research coordination perceptions of a coached home spirometry protocol: ongoing experiences with the OUTREACH study
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: G. Sawicki, J. Greenberg, N. Reid, B. Fogarty, N. Midamba, A. Berlinski, M. Rosenfeld, A. Hartzler Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
119 Interim results of test reliability of 19F MRI in mild cystic fibrosis lung disease
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: J. Goralski, S. Chung, M. Powell, A. Ceppe, Y. Lee, S. Donaldson Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
121 Longitudinal MRI of morphological and perfusion abnormalities in children with cystic fibrosis from infancy to end of adolescence
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: M. Wielputz, S. Triphan, L. Wucherpfennig, P. Leutz-Schmidt, S. Gestewitz, E. Steinke, S. Graeber, H. Kauczor, M. Eichinger, M. Puderbach, A. Alrajab, J. Schenk, O. Sommerburg, M. Stahl, M. Mall Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
122 Pharmacodynamic effects of brensocatib in people with cystic fibrosis
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: J. Tolle, E. DiMango, M. Konstan, C. Ramirez, J. Flarakos, J. Basso, S. Li, A. Teper, H. Usansky, M. Vergara Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
123 Rates of change in growth, body composition, muscle strength, and FEV1 during elexacaftor-tezacaftor-ivacaftor therapy for 6- to 11-yearold children
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: T. Boat, W. Hardie, M. Hossain, A. Nakamura, C. Dress, M. Hjelm Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
124 Is home spirometry accurate? Comparison between home and office spirometry in the PROMISE study
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: M. Rosenfeld, C. O ’Rourke, P. Vu, A. De Fermin Cortes, A. Kelly, D. Nichols, J. Pittman, F. Ratjen, G. Solomon, N. Hamblett, S. Heltshe Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
125 Therapeutic drug monitoring system for CFTR modulators and their respective potent metabolites using high-performance liquid chromatography
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: R. Willey Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
126 A phase 1b/2a randomized, double-blind, placebo-controlled, multicenter study evaluating nebulized phage therapy in people with cystic fibrosis with chronic Pseudomonas aeruginosa pulmonary infection
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: U. Rappo, M. Kahan-Hanum, X. Ussery, E. Kario, H. Nevenzal, I. Weiner, H. Sberro Livnat, T. Gera, J. Jablonska, N. Buchshtab, T. Axelrod, O. Bahar, V. Lev, Y. Tzur, Y. Zarchin, M. Golembo, R. Vilchez, E. Kerem, M Bassan Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
127 Dual delivery microbial enzymatic product as alternative pancreatic enzyme replacement therapy for people with cystic fibrosis
(Source: Journal of Cystic Fibrosis)
Source: Journal of Cystic Fibrosis - October 1, 2023 Category: Respiratory Medicine Authors: M. Poza, B. Nasreddine Tags: CLINICAL TRIALS & OUTCOME MEASURES Source Type: research
