Bowel perforation from malignant atrophic papulosis treated with eculizumab

We present the case of a 57-year-old man with known cutaneous manifestations of malignant atrophic papulosis, also known as Köhlmeier-Degos disease, who developed an almost-fatal small bowel perforation following a parathyroidectomy. He required two surgical interventions during his initial hospitalization and was started on eculizumab. Despite these therapies, the patient developed recurrent bowel perforations and ultimately died.PMID:33456165 | PMC:PMC7785204 | DOI:10.1080/08998280.2020.1809942

Source: Baylor University Medical Center Proceedings - January 18, 2021 Category: Universities & Medical Training Authors: Ajithraj Sathiyaraj Priyanga Jayakumar Matthew R McGlennon John F Eckford Sandy Itwaru Anne Source Type: research