Acrofacial dysostosis suggesting Nager syndrome in newborn – Diagnostic and therapeutic difficulties
Conclusions: Nager syndrome is a rare disease with craniofacial and preaxial limb involvement. The quality of life of patients with Nager syndrome can be improved by an early diagnosis. A proper prenatal screening allows to perform differential diagnosis (from Treacher Collins, Miller, Pierre-Robin sequence and Roberts syndromes) before birth and prepare the parents for the upcoming challenges. (Source: Pediatria Polska)
Source: Pediatria Polska - April 21, 2017 Category: Pediatrics Source Type: research

Longitudinal observations on growth patterns of obese infants: Developing country perspectives. Preliminary study
Conclusions The growth patterns of obese infants suggest a trend of higher BMIs persisting into childhood. Larger studies are required to confirm these findings. (Source: Pediatria Polska)
Source: Pediatria Polska - April 19, 2017 Category: Pediatrics Source Type: research

Dr med. Kazimierz Bartkowiak (1921 –2007) Wspomnienie w 10. rocznicę śmierci
Publication date: Available online 17 April 2017 Source:Pediatria Polska (Source: Pediatria Polska)
Source: Pediatria Polska - April 18, 2017 Category: Pediatrics Source Type: research

Ocena spo życia wód smakowych przez dzieci kierowane do oddziału pediatryznego
Conclusion A large percent of parents perceive flavored water as a healthy drink in their children's diets. There is a strong need for parental education about the potential adverse effects of those beverages on the child's health. (Source: Pediatria Polska)
Source: Pediatria Polska - April 14, 2017 Category: Pediatrics Source Type: research

Heterogenno ść kliniczna zespołu Kabuki (zespół Niikawy i Kurokiego) na podstawie opisu przypadku15-letniej pacjentki z nawykowym zwichnięciem rzepek
Publication date: Available online 13 April 2017 Source:Pediatria Polska Author(s): Michał Błoch, Robert Śmigiel Kabuki Syndrome (KS) is a rare genetic disease affecting about 1 in 30,000−86,000 live births. KS is characterized by the appearance of the distinctive dysmorphic features and coexisting congenital disorders. The majority of patients are diagnosed with mild and moderate intellectual disabilities. The clinical picture of the KS consists of skeletal disorders, for example, joints hypermobility. One such described patient shows intellectual norm which allows her to be educated in public school with the st...
Source: Pediatria Polska - April 14, 2017 Category: Pediatrics Source Type: research

80-lecie fenyloketonurii. Cz ęść IV: Stanisław F. Śnieszko i Ada J. Susi a historia opracowania testu Guthriego
Publication date: Available online 17 February 2017 Source:Pediatria Polska Author(s): Kamil K. Hozyasz The aim of this paper was to provide information on remarkable influence of scientists, who emigrated from the East Europe in to the USA, in the entire field of the Guthrie test invention. While working as graduate assistant at the University of Maine, Robert Guthrie trained in bacteriology with Dr. Stanislas F. Snieszko (1902–1984), “who turned out to be an influential person in his life” (as was stated in Guthrie's biography by JH Koch). Snieszko was born in Krzyz, Poland. He graduated in Jagiellonia...
Source: Pediatria Polska - April 13, 2017 Category: Pediatrics Source Type: research

Mid cavity complete transverse vaginal septum: Ultrasound diagnoses and management
Conclusion Hematocolpos is a sequel of distal outlet obstruction. Transverse vaginal septum can be seen on ultrasound evaluating its thickness, assessing its level and excluding distal vaginal atresia. (Source: Pediatria Polska)
Source: Pediatria Polska - April 13, 2017 Category: Pediatrics Source Type: research

Long-term clinical effects of enzyme replacement therapy in MPS II
We report clinical results of long-term enzyme replacement therapy in Polish population of patients with mucopolysaccharidosis type II (MPS II). The therapy was deemed ineffective and was discontinued in the majority of them but reaching the consensus on ineffectiveness of enzyme replacement required often several years. The standard clinical monitoring parameters such as: six-minute walking test, pulmonary function tests, severity of organomegaly and of heart dysfunction, proved to be hardly helpful in many cases. This was caused by young age of patients, their physical and intellectual disabilities as well as by various ...
Source: Pediatria Polska - April 12, 2017 Category: Pediatrics Source Type: research

First experience with biodegradable airway stents in children – Case report
Publication date: Available online 8 April 2017 Source:Pediatria Polska Author(s): Andrzej Zając, Mirosław Krysta, Przemysław Tomasik, Wojciech Górecki Airway malacia is the most common cause of tracheobronchial obstruction in children. It can be congenital or acquired. Aortopexy and surgical relief of external compression are main therapeutical options. An alternative for surgical approach can be metallic airway stents, but usually they are not considered as a first choice, because of relatively high risk of complications. Moreover, metallic airway stents are permanent, so they have limited usage in growing bro...
Source: Pediatria Polska - April 11, 2017 Category: Pediatrics Source Type: research

Congenital hepatic fibrosis associated with Gilbert's syndrome and cholelithiasis in a pediatric patient – The crucial role of liver biopsy in diagnostic process
We report an undescribed so far coexistence of biopsy proven congenital hepatic fibrosis with cholelithiasis and Gilbert's syndrome in a pediatric patient. (Source: Pediatria Polska)
Source: Pediatria Polska - April 11, 2017 Category: Pediatrics Source Type: research

Neonatal duodenal obstruction due to a preduodenal portal vein associated with intestinal malrotation: A case report
We report a full term 16-day-old girl who presented with recurrent non-bilious vomiting soon after birth. Clinically, she was dehydrated and the abdomen was not distended. Abdominal radiography showed a dilated stomach and the first part of duodenum with some gas in the distal intestines. Abdominal ultrasound revealed distended stomach, dilatation of proximal duodenum and intestinal malrotation. Upper gastrointestinal contrast study showed severe gastroesophageal reflux with delayed passage of contrast to the small bowel, distended stomach and proximal duodenum confirming partial duodenal obstruction. Surgical exploration ...
Source: Pediatria Polska - April 11, 2017 Category: Pediatrics Source Type: research

Por ównanie laryngoskopii bezpośredniej i wideolaryngoskopii podczas symulowanego unieruchomienia odcinka szyjnego kręgosłupa u dziecka
Conclusions In simulation study, it has been demonstrated that the use of the stabilization of the cervical spine significantly reduces the effectiveness of endotracheal intubation. Persons participating in the study performed intubation using GlideScope video-laryngoscopy with more efficiency at first attempt intubation and in less time. Further research is needed to confirm the results. (Source: Pediatria Polska)
Source: Pediatria Polska - April 11, 2017 Category: Pediatrics Source Type: research

Button battery ingestion as a life threatening condition in pediatric practice
Publication date: Available online 8 April 2017 Source:Pediatria Polska Author(s): Marek Boba, Katarzyna Lipka, Małgorzata Partyka, Joanna Majzel, Ewa Gacka Foreign body ingestion is common, especially among children aged 6 months to 3 years old. The button battery represents about 2% of foreign bodies swallowed by children, relative frequency of its ingestion is increasing. About 30% of children with esophageal foreign body will be asymptomatic. Button batteries larger than 20mm, if remains in the esophagus, may lead to gastrointestinal tract damages. The final damaging effect of disc battery follows the type of swollen...
Source: Pediatria Polska - April 11, 2017 Category: Pediatrics Source Type: research

Errata do artyku łu: Stała stymulacja serca u dzieci – wskazania, techniki implantacji oraz powikłania [Pediatria Polska 2017; 92(2):178–184]
Publication date: Available online 9 April 2017 Source:Pediatria Polska Author(s): Aneta Maria Polewczyk, Maciej Polewczyk, Andrzej Kutarski, Anna Polewczyk (Source: Pediatria Polska)
Source: Pediatria Polska - April 11, 2017 Category: Pediatrics Source Type: research

Zastosowanie metody wyp łukiwania gazów w diagnostyce czynnościowej płuc u dzieci
Publication date: Available online 24 March 2017 Source:Pediatria Polska Author(s): Maria Wawszczak, Joanna Peradzyńska The inert gas washout (IGW) is a noninvasive measurement applicable in evaluation of peripheral airway function. This technique offers information about pulmonary ventilation inhomogeneity and provides insight into the evolution of pathological processes by assessing the efficiency of inert gases washout. The method can be performed by two techniques: single breath washout (SBW) test which involves a vital capacity maneuvers and over a series of tidal breathes termed a multiple breath washout test (MBW)...
Source: Pediatria Polska - April 5, 2017 Category: Pediatrics Source Type: research

Choroba Fabry ’ego u członków jednej rodziny − trudności diagnostyczne związane z polimorfizmem genowym
Publication date: Available online 4 April 2017 Source:Pediatria Polska Author(s): Joanna Bielak, Elżbieta Czyżyk, Agnieszka Ługowska, Anna Tylki-Szymańska Fabry disease is a rare lysosomal disease, inherited in the X-linked manner. It is caused by a mutation in the gene GLA locus Xq22 which results in a deficiency of the enzyme α -galactosidase and deposition of globotriaosylceramide (GL3) in the tissues and organs of patients. Its prevalence is estimated at 1:40 000–1:120 000 live male births. The women who carry the mutation rarely remain asymptomatic. The majority of symptoms characteristic of Fabry di...
Source: Pediatria Polska - April 5, 2017 Category: Pediatrics Source Type: research

Ocena spo życia wód smakowych przez dzieci kierowane do oddziału pediatrycznego
Conclusion A large percent of parents perceive flavored water as a healthy drink in their children's diets. There is a strong need for parental education about the potential adverse effects of those beverages on the child's health. (Source: Pediatria Polska)
Source: Pediatria Polska - April 5, 2017 Category: Pediatrics Source Type: research

Button battery aspiration in children: Our experiences in a tertiary care teaching hospital of eastern India
Conclusion Early detection of such foreign bodies is essential to safe removal. Management approach has to be systematic. Preoperative history taking, radiological assessment followed by rapid intervention by skilled bronchoscopist usually results in favorable outcome. (Source: Pediatria Polska)
Source: Pediatria Polska - April 4, 2017 Category: Pediatrics Source Type: research

Co nowego w cholestazie – część 3. Wrodzone zaburzenia syntezy kwasów żółciowych
Publication date: Available online 3 April 2017 Source:Pediatria Polska Author(s): Patryk Lipiński, Piotr Socha, Irena Jankowska Cholestatic liver diseases remain a major clinical issue for pediatricians. The article constitutes an up-to-day overview on the inborn errors of bile acids synthesis. (Source: Pediatria Polska)
Source: Pediatria Polska - April 4, 2017 Category: Pediatrics Source Type: research

Mid cavity transverse vaginal septum: Ultrasound diagnoses
Conclusion Hematocolpos is a sequel of distal outlet obstruction. Transverse vaginal septum can be seen and measured in thickness on ultrasound and exclude distal atresia by ultrasound. (Source: Pediatria Polska)
Source: Pediatria Polska - April 4, 2017 Category: Pediatrics Source Type: research

Assessment of nutritional habits and nutrition status in patients with Crohn's disease before Exclusive Enteral Nutrition and after gaining remission
Conclusion As a result of the implemented therapy, body mass increase was noted in all children. The research shows that a diet used in the remission is improper in terms of energy intake same nutrients which involves the risk of qualitative insufficiencies. (Source: Pediatria Polska)
Source: Pediatria Polska - April 4, 2017 Category: Pediatrics Source Type: research

Stulecie urodzin Profesor Marii Goncerzewicz. Pozna ński okres jej działalności kliniczno-naukowej i organizacyjnej
Publication date: Available online 4 April 2017 Source:Pediatria Polska Author(s): Marian Krawczyński On the occasion of the birth centenary of Professor Maria Goncerzewicz, her biography and organizational and scientific achievements in pediatrics are presented. Her university studies and over 20 years of her professional career took place at Poznań University of Medical Sciences. Her clinical and scientific activity in the area of metabolic disorders, especially PKU, is presented. Many of her publications were dedicated to the interface between clinical genetics and pediatric endocrinology as well as social pediatrics...
Source: Pediatria Polska - April 4, 2017 Category: Pediatrics Source Type: research

Fungal laryngitis in asthmatic boy treated with inhalatory corticosteroids: A case report
This report describes the case of a 12-year-old boy with chronic bronchial asthma receiving prolonged inhaled corticosteroids presented with progressive hoarseness of voice. Patient had undergone microlaryngeal surgery with stripping of the vocal cords. Histopathology demonstrated hyperplastic ulcerative squamous epithelium with fungal hyphae and confirmed as Aspergillus. This is an extremely rare side effect of prolonged inhalation of corticosteroids in a pediatric patient. (Source: Pediatria Polska)
Source: Pediatria Polska - April 4, 2017 Category: Pediatrics Source Type: research

Program Szczepie ń Ochronnych w 2017 roku − powszechne szczepienia przeciwko pneumokokom u dzieci
Publication date: Available online 28 March 2017 Source:Pediatria Polska Author(s): Teresa Jackowska, Ewa Bernatowska In Poland, starting from 2017, mandatory vaccination against pneumococcus in children will be financed. There are two conjugate vaccines: PCV10 and PCV13 for children from 2 months of age. PCV10 vaccine was purchased for mandatory vaccination programme. In 2011−2015, PCV13 vaccine in children provided more than 20% broader serotypes coverage than the PCV10 vaccine (www.koroun.edu.pl). PCV13 is the only vaccine that demonstrated protection against invasive and non-invasive diseases caused by serotype ...
Source: Pediatria Polska - March 29, 2017 Category: Pediatrics Source Type: research

Łagodna nawracająca cholestaza wewnątrzwątrobowa
Publication date: Available online 28 March 2017 Source:Pediatria Polska Author(s): Patryk Lipiński, Joanna Pawłowska, Irena Jankowska The article constitutes an up-to-day overview on pathogenesis, clinical manifestation and treatment of benign recurrent intrahepatic cholestasis in children. (Source: Pediatria Polska)
Source: Pediatria Polska - March 29, 2017 Category: Pediatrics Source Type: research

W łaściwości psychometryczne polskiej adaptacji kwestionariusza oceny zadowolenia rodziców z ambulatoryjnej opieki pediatrycznej
Conclusion Providing high quality medical services requires direct reference to the practitioner (patients and their families) through reliable measurement of satisfaction with health care. The Polish version of the Kinder ZAP questionnaire can be used to measure the satisfaction of outpatient pediatric care both from the perspective of the parent and the child. (Source: Pediatria Polska)
Source: Pediatria Polska - March 28, 2017 Category: Pediatrics Source Type: research

Szczepienia u dzieci z chorob ą nowotworową − aktualne polskie zalecenia
Publication date: Available online 27 March 2017 Source:Pediatria Polska Author(s): Ewelina Gowin, Danuta Januszkiewicz-Lewandowska, Teresa Jackowska, Jarosław Peregud-Pogorzelski, Jacek Wysocki The article presents, in accordance with current recommendations of the Infectious Diseases Society of America (IDSA) and the Programme of Immunization 2017 (PSO), proposals for the implementation of vaccination in children with cancer, depending on the applied treatment. We recommend to start vaccination 6 months after the end of cancer treatment, which is consistent with the guidelines of the IDSA. After vaccination with a live...
Source: Pediatria Polska - March 28, 2017 Category: Pediatrics Source Type: research

Zastosowanie metody wyp łukiwania gazów w praktyce pediatrycznej
Publication date: Available online 24 March 2017 Source:Pediatria Polska Author(s): Maria Wawszczak, Joanna Peradzyńska The inert gas washout (IGW) is a noninvasive measurement applicable in evaluation of peripheral airway function. This technique offers information about pulmonary ventilation inhomogeneity and provides insight into the evolution of pathological processes by assessing the efficiency of inert gases washout. The method can be performed by two techniques: single breath washout (SBW) test which involves a vital capacity maneuvers and over a series of tidal breathes termed a multiple breath washout test (MBW)...
Source: Pediatria Polska - March 25, 2017 Category: Pediatrics Source Type: research

Chylothorax and necrotizing pneumonia as complications of vomiting and cough induced by placement of a gastric tube for enteral nutrition in a 8-year old boy with Crohn's disease
Publication date: Available online 25 March 2017 Source:Pediatria Polska Author(s): Wronowski Michał, Kotowska Maria, Krenke Katarzyna, Albrecht Piotr A boy aged 8, with chronic diarrhoea, was admitted to clinic for diagnosis of Crohn's disease. The diagnosis was confirmed and total enteral nutrition initiated. Due to intolerance of oral intake, it was decided to insert gastric tube for nutrition. Two attempts of insertion were unsuccessful due to stubborn vomiting and cough – only minor amount of polymeric diet was administered. During next 24 hours the general state of patient worsened sharply. Dyspnoea and tachy...
Source: Pediatria Polska - March 25, 2017 Category: Pediatrics Source Type: research

Dysembrioplastyczny guz nerwowo-nab łonkowy (DNT) u 9-letniego chłopca – od objawu do rozpoznania
We describe the conducted differential diagnosis including disorders of calcium-phosphate metabolism, seizure disorders, ischaemic changes and organic changes in the central nervous system. The paper also discusses differentiation of tetany and partial seizures associated with the presence of a tumour in the central nervous system. The patient was diagnosed with epilepsy which, despite partial tumour removal, needs further pharmacological treatment. The management strategy for this case of drug-resistant epilepsy caused by DNT localised in the eloquent brain area is presented. (Source: Pediatria Polska)
Source: Pediatria Polska - March 25, 2017 Category: Pediatrics Source Type: research

Dr med. Jolanta Pie ńkowska-Mikołajczyk (1927−1996) − pediatra, pionier poznańskiej endokrynologii dziecięcej. Wspomnienie
Publication date: Available online 25 March 2017 Source:Pediatria Polska Author(s): Marian Krawczyński The biography of Jolanta Pieńkowska-Mikołajczyk MD, PhD, an universally educated pediatrician of Poznań is presented. In particular, the traits of her personality, professional way and scientific achievements in a new, developing area – pediatric endocrinology – are depicted. She was professionally active from the fifties to the eighties of the 20th century. (Source: Pediatria Polska)
Source: Pediatria Polska - March 25, 2017 Category: Pediatrics Source Type: research

Analiza zmian chorobowych przydatk ów u dziewczynek leczonych operacyjnie
Conclusion Adnexal lesions requiring surgical treatment in adolescent are mostly unilateral benign ovarian cysts. The type of surgery (laparoscopy/laparotomy) mainly depends on the size and nature of an adnexal lesion. (Source: Pediatria Polska)
Source: Pediatria Polska - March 24, 2017 Category: Pediatrics Source Type: research

Zmiany st ężeń waspiny i leptyny w surowicy u noworodków donoszonych z wrodzonym zapaleniem płuc
Conclusions 1. Congenital pneumonia in full-term AGA neonates contributes to increase of serum vaspin and leptin concentrations, independently of their gender, birth weight, birth asphyxia and type of delivery. 2. Healthy full-term female neonates have significantly higher vaspin and leptin concentrations than the male neonates. 3. In healthy and pneumonic neonates, any significant correlation between serum vaspin and leptin concentrations and body length, head and chest circumferences, and any mutual correlation between vaspin and leptin were stated. (Source: Pediatria Polska)
Source: Pediatria Polska - March 23, 2017 Category: Pediatrics Source Type: research

Co nowego w cholestazie – część 1. Cholestaza z prawidłową aktywnością gamma-glutamylotranspeptydazy
Publication date: Available online 7 March 2017 Source:Pediatria Polska Author(s): Patryk Lipiński, Irena Jankowska Cholestatic liver diseases remain a major clinical issue for pediatricians. The article constitutes an up-to-date overview on cholestasis with normal serum gamma-glutamyl transpeptidase activity. The authors presented the pathogenicity, clinical presentation, biochemical and molecular diagnostics of the following disorders: citrin deficiency, progressive familial intrahepatic cholestasis type 4, cholestasis associated with FXR mutations, familial hypercholanemia, cholestasis associated with MYO5B mutations ...
Source: Pediatria Polska - March 7, 2017 Category: Pediatrics Source Type: research

Zesp ół szkliwno-nerkowy (ERS) – charakterystyczne objawy w jamie ustnej
Publication date: Available online 2 March 2017 Source:Pediatria Polska Author(s): Weronika Jończyk, Barbara Bartosiak-Drosio, Halszka Boguszewska-Gutenbaum, Dorota Olczak-Kowalczyk Amelogenesis imperfecta (AI; congenital enamel hypoplasia) is a genetic disorder of developmental enamel of ectodermal origin that relates to the enamel of deciduous (primary) and permanent teeth. Recent reports suggested that Amelogenesis imperfecta may be associated with morphological and biochemical changes elsewhere in the body. The clinical features of Amelogenesis imperfecta vary depending on the type. In the hypoplastic type of Ameloge...
Source: Pediatria Polska - March 1, 2017 Category: Pediatrics Source Type: research

Karmienie piersi ą a próchnica wczesnego dzieciństwa – systematyczny przegląd piśmiennictwa
Conclusions Basing on performed analysis the time of weaning to reduce the risk of early childhood caries cannot be accurately defined. However, in the presence of maxillary incisors it should be advised to limit the breastfeeding at night and before daytime naps and tooth brushing after a meal should be recommended to overcome potential cariogenicity of human milk in the case of reduced secretion of saliva during sleep. (Source: Pediatria Polska)
Source: Pediatria Polska - February 16, 2017 Category: Pediatrics Source Type: research

Co nowego w cholestazie – część 2. Cholestaza z podwyższoną aktywnością gamma-glutamylotranspeptydazy
Publication date: Available online 17 February 2017 Source:Pediatria Polska Author(s): Patryk Lipiński, Irena Jankowska Cholestatic liver diseases remain a major clinical issue for pediatricians. The article constitutes an up-to-day overview on cholestasis with elevated serum gamma-glutamyl transpeptidase activity. Authors presented the pathogenicity, clinical presentation, biochemical and molecular diagnostics of the following disorders: progressive familial intrahepatic cholestasis type 3, adenosine kinase deficiency, neonatal ichthyosis – sclerosing cholangitis syndrome. (Source: Pediatria Polska)
Source: Pediatria Polska - February 16, 2017 Category: Pediatrics Source Type: research

Wrodzone zaro śnięcie krtani i przełyku u dziewczynki z delecją 22q11.2 – opis przypadku
We report on the case of 3.5-year-old girl with DGS, esophageal and laryngeal atresia because of the rarity of this combination and for the purpose to underline the role of early endoscopic examination of airways, especially before surgery in this group of patients. (Source: Pediatria Polska)
Source: Pediatria Polska - February 16, 2017 Category: Pediatrics Source Type: research

80-lecie fenyloketonurii. Cz ęść IV: Stanisław F. Snieszko i Ada J. Susi a historia opracowania testu Guthriego
Publication date: Available online 17 February 2017 Source:Pediatria Polska Author(s): Kamil K. Hozyasz The aim of this paper was to provide information on remarkable influence of scientists, who emigrated from the East Europe in to the USA, in the entire field of the Guthrie test invention. While working as graduate assistant at the University of Maine, Robert Guthrie trained in bacteriology with Dr. Stanislas F. Snieszko (1902–1984), “who turned out to be an influential person in his life” (as was stated in Guthrie's biography by JH Koch). Snieszko was born in Krzyz, Poland. He graduated in Jagiellonia...
Source: Pediatria Polska - February 16, 2017 Category: Pediatrics Source Type: research

Zaka żenia narządów płciowych u dziewcząt – profilaktyka i leczenie
Publication date: Available online 7 February 2017 Source:Pediatria Polska Author(s): Agnieszka Drosdzol-Cop, Agnieszka Białka, Igor Bakon, Violetta Skrzypulec-Plinta Genital infections are a frequent diagnosis in pediatric and adolescent gynecology out-patient clinics, 2/5 of which relate to girls aged 0–14 years. The course of disease ranging from symptoms and ending on the treatment depends on many factors, foremost of the infection pathogen, but also on the child's age, coexisting diseases and sexual activity. Genital infections in girls can be caused by bacteria, viruses, fungi, parasites or factors of non-com...
Source: Pediatria Polska - February 15, 2017 Category: Pediatrics Source Type: research

Paracetamol jako alternatywna metoda leczenia hemodynamicznie istotnego PDA u noworodk ów urodzonych przedwcześnie – wstępne wyniki badań
Conclusions Paracetamol can be used as an alternative method of treatment of hsPDA to ibuprofen. (Source: Pediatria Polska)
Source: Pediatria Polska - February 15, 2017 Category: Pediatrics Source Type: research

Zasady stosowania kom ór inhalacyjnych u dzieci
Publication date: Available online 16 February 2017 Source:Pediatria Polska Author(s): Andrzej Emeryk, Zbigniew Doniec, Henryk Mazurek, Katarzyna Krenke, Michał Pirożyński, Tomasz Sosnowski, Emil Florkiewicz Experts of four scientific societies and the independent experts described the position paper concerning the role of inhalation chambers in inhalation therapy in children. This document is directed to all paediatricians and family doctors. We have reviewed the most important original and review papers, together with an analysis of the holding chambers market in the country. Recommendations containing indications an...
Source: Pediatria Polska - February 15, 2017 Category: Pediatrics Source Type: research

Risk factors of periventricular leukomalacia in singleton infants born from 23rd to 26th weeks of gestation – Retrospective study
Conclusions Delivery in the third-level hospital as well as IVH prevention significantly reduces the risk of PVL. Well-developed prenatal care, fetus transport in utero and delivery in the third-level hospital seem to be crucial in the prevention of this pathology. (Source: Pediatria Polska)
Source: Pediatria Polska - February 14, 2017 Category: Pediatrics Source Type: research

Wp ływ wczesnych zakażeń na stężenie adiponektyny i leptyny w surowicy noworodków donoszonych
Conclusions 1. Early-onset infections in full-term eutrophic newborns contribute to increase of adiponectin and leptin concentrations, independently of their gender, birth asphyxia and type of delivery. 2. In infected newborns any significant correlations between adiponectin concentrations and birth weight, body length, chest and head circumferences were noted. (Source: Pediatria Polska)
Source: Pediatria Polska - February 9, 2017 Category: Pediatrics Source Type: research

Large patent ductus arteriosus and left ventricular non-compaction as cardiac manifestations of 1p36 monosomy
We describe an infant with dysmorphic features and two different cardiac anomalies (patent ductus arteriosus and left ventricular non-compaction) in which monosomy 1p36 was recognized. (Source: Pediatria Polska)
Source: Pediatria Polska - February 8, 2017 Category: Pediatrics Source Type: research

Karmienie piersi ą a próchnicą wczesnego dzieciństwa – systematyczny przegląd piśmiennictwa
Conclusions Basing on performed analysis the time of weaning to reduce the risk of tooth decay cannot be accurately defined. However, in the presence of maxillary incisors it should be advised to limit the breastfeeding at night and before daytime naps and tooth brushing of after a meal should be recommended to overcome potential cariogenicity of milk in the case of reduced secretion of saliva during sleep. (Source: Pediatria Polska)
Source: Pediatria Polska - February 6, 2017 Category: Pediatrics Source Type: research

Infekcje narz ądów płciowych u dziewcząt – profilaktyka i leczenie
Publication date: Available online 7 February 2017 Source:Pediatria Polska Author(s): Agnieszka Drosdzol-Cop, Agnieszka Białka, Igor Bakon, Violetta Skrzypulec-Plinta Genital infections are a frequent diagnosis in pediatric and adolescent gynecology out-patient clinics, 2/5 of which relate to girls aged 0–14 years. The course of disease ranging from symptoms and ending on the treatment depends on many factors. Foremost of the infection pathogen, but also on the child's age, coexisting diseases and sexual activity. Genital infections in girls can be caused by bacteria, viruses, fungi, parasites or factors of non-com...
Source: Pediatria Polska - February 6, 2017 Category: Pediatrics Source Type: research

Rapid strip tests as a decision-making tool about antibiotic treatment in children – A prospective study
Conclusions Rapid diagnostic tests used by the family physicians in initial diagnostics of seasonal upper respiratory tract infections in children allowed to differentiate between the type of infection as well as reduce the number of follow-up visits. Also, the antibiotic spending reimbursed by the insurer decreased by 17%. (Source: Pediatria Polska)
Source: Pediatria Polska - February 6, 2017 Category: Pediatrics Source Type: research

R óżny przebieg kliniczny rozsianego krzepnięcia wewnątrznaczyniowego (DIC) w okresie ustalania rozpoznania ostrej białaczki monoblastycznej (AML-M5) u 2 dzieci
We present two children with AML-M5 and rearrangement of the MLL gene, treated according to BFM AML 98 Interimphase 2004 and BFM AML 2012 protocol. The first patient had laboratory signs of DIC as undetectable (below quantifiable levels of) coagulation parameters without any clinical symptoms diagnosed at the same time as leukemia and persistent during the induction chemotherapy. The second patient had changes first in the coagulogram on the second day of induction chemotherapy. In the subsequent days, major bleeding from mucous membranes of the oral cavity, requiring intensive substitute treatment, was observed. The highe...
Source: Pediatria Polska - February 4, 2017 Category: Pediatrics Source Type: research

Wewn ątrzotrzewnowo położona torbiel bronchogenna u dziecka – niezwykle rzadka wada wrodzona – opis przypadku i przegląd piśmiennictwa
Publication date: Available online 23 January 2017 Source:Pediatria Polska Author(s): Michał Jerzy Pasierbek, Wojciech Korlacki, Andrzej Grabowski, Maciej Ilewicz Bronchogenic cyst is a congenital tumor resulting from abnormal development of the foregut. Most described cysts are located in the mediastinum, giving symptoms of respiratory infection. Isolated intra-abdominal bronchogenic cyst is a rare abnormality, usually located retroperitoneally. In such a location, they are mostly asymptomatic until secondary infection or achieving a size capable of causing pressure on the important anatomical structures. Once the diagn...
Source: Pediatria Polska - January 23, 2017 Category: Pediatrics Source Type: research