Modified Ravitch Procedure for Left Poland Syndrome Combined With Pectus Excavatum.

Modified Ravitch Procedure for Left Poland Syndrome Combined With Pectus Excavatum. Ann Thorac Surg. 2017 Oct;104(4):e337-e339 Authors: Cortés-Julián G, Bushra-Nuritu HB, Buenfil-Fuentes R, Merino Rajme JA Abstract Poland Syndrome is a rare disease with an incidence of 1 in 30,000. This disease is characterized by agenesis of the pectoralis major, hypoplasia of mammarian tissue and the nipple complex, and limb abnormalities. The severe form of this disease can be associated with rib and sternal malformations like pectus excavatum. A 19-year-old man with severe Poland syndrome with cardiac extrasystoles and restrictive ventilation as shown by a spirometry test is presented. A total sternal reconstruction with partial osteotomies and bilateral resection of cartilage was performed. The sternum was stabilized with underlying titanium bars and clips. The cosmetic result was satisfactory. PMID: 28935331 [PubMed - in process]
Source: The Annals of Thoracic Surgery - Category: Cardiovascular & Thoracic Surgery Authors: Tags: Ann Thorac Surg Source Type: research