Rosai Dorfman Disease: A Rare Case Report
AbstractTo study the presentation and plan of treatment of patient with Rosai Dorfman Disease. Rosai-Dorfman disease(RDD), is rare, non-neoplastic, multisystemic histiocytic disorder. Nodal form is more common. It ’s self-limiting disorder of unknown etiology. Symptomatic treatment is mainstay. Bardet–Biedl syndrome (BBS) is rare ciliopathic, autosomal-recessive disorder, affecting multiple organs. Characterized by marked central obesity, retinal dystrophy, polydactyly, mental retardation, hypogonadism an d renal dysfunction. Treatment is symptomatic with hormone supplementation& regular follow-ups. 10 year male ...
Source: Indian Journal of Otolaryngology and Head and Neck Surgery - December 11, 2023 Category: ENT & OMF Source Type: research
Facial Cutaneous Rosai-Dorfman Disease: Dermoscopic Findings with Successful Surgical Treatment
Ann Dermatol. 2023 Nov;35(Suppl 2):S287-S291. doi: 10.5021/ad.22.071.ABSTRACTRosai-Dorfman disease (RDD) is a rare non-Langerhans cell histiocytosis characterized by an accumulation of activated histiocytes within the affected tissues. It is a heterogeneous disease that includes the classical (nodal) and extra-nodal variants. The cutaneous form of the disease without the characteristic lymphadenopathy is rare and is often misdiagnosed as other dermatologic diseases. Misdiagnosis as lymphoproliferative and infectious diseases such as lymphoma and tuberculosis have been reported in the literature. Herein, we report a case of...
Source: Annals of Dermatology - December 7, 2023 Category: Dermatology Authors: Keunyoung Hur Ji Yeon Hong Kyu Han Kim Jihui Jeon Cheol Lee Yoonjin Kwak Tae Min Kim Je-Ho Mun Source Type: research
Investigating the correlation between small molecular inhibitor utilization, peripheral blood monocytes, and treatment outcomes in Rosai Dorfman disease
This study is the largest analysis of Rosai Dorfman disease, that we are aware of, from a single inst itution. In this cohort, the utilization of small molecule inhibitors corresponded to a greater increase in partial responses than conventional therapies, although the opposite effect has been observed in complete responses. This finding can be attributed to the recent introduction of targeted agent s and shorter follow-up. We anticipate higher complete response rates with the use of small molecule in ongoing analyses over a longer follow-up period. The recognition of relative monocyte elevation prior to disease progressio...
Source: Annals of Hematology - November 9, 2023 Category: Hematology Source Type: research
Neurological syndromes and potential triggers associated with antibodies to neuronal surface antigens
CONCLUSION: We identified seasonal variability associated with neuronal surface antibodies suggesting environmental triggers. Also, we described the coexistence of NMDAr-IgG encephalitis with histiocytosis. In our series, most patients received second-line immunotherapy. We observed neurologic improvement after treatment even in cases of delayed diagnosis. Increasing the recognition and availability of tests and treatments for these conditions is of paramount importance in low- and middle-income countries.PMID:37864878 | DOI:10.1016/j.msard.2023.105022 (Source: Herpes)
Source: Herpes - October 21, 2023 Category: Infectious Diseases Authors: Bruna Klein da Costa Paula de Oliveira Pinto Lia Staub Gisele Hansel Guilherme Vanik Pinto Lucas Porcello Schilling Giordani Rodrigues Dos Passos William Alves Martins Jefferson Becker Raphael Machado Castilhos Andr é Palmini Douglas Kazutoshi Sato Source Type: research
Neurological syndromes and potential triggers associated with antibodies to neuronal surface antigens
CONCLUSION: We identified seasonal variability associated with neuronal surface antibodies suggesting environmental triggers. Also, we described the coexistence of NMDAr-IgG encephalitis with histiocytosis. In our series, most patients received second-line immunotherapy. We observed neurologic improvement after treatment even in cases of delayed diagnosis. Increasing the recognition and availability of tests and treatments for these conditions is of paramount importance in low- and middle-income countries.PMID:37864878 | DOI:10.1016/j.msard.2023.105022 (Source: Herpes)
Source: Herpes - October 21, 2023 Category: Infectious Diseases Authors: Bruna Klein da Costa Paula de Oliveira Pinto Lia Staub Gisele Hansel Guilherme Vanik Pinto Lucas Porcello Schilling Giordani Rodrigues Dos Passos William Alves Martins Jefferson Becker Raphael Machado Castilhos Andr é Palmini Douglas Kazutoshi Sato Source Type: research
Letter to the Editor: "Rosai Dorfman: Rare Cause of Cervical Lymphadenopathy"
Ear Nose Throat J. 2023 Oct 16:1455613231205538. doi: 10.1177/01455613231205538. Online ahead of print.ABSTRACTWe read with great interest the article by Kobayashi KE et al. published in 2023 entitled: "Presentation of external ear Rosai-Dorfman disease with laryngeal involvement" and wish to reconnoiter Rosai-Dorfman Disease's (RDD) clinical entities and the possible implications from the perspective of otology.PMID:37843046 | DOI:10.1177/01455613231205538 (Source: Ear, Nose and Throat Journal)
Source: Ear, Nose and Throat Journal - October 16, 2023 Category: ENT & OMF Authors: Muhammad Raziin Zainal Abidin Geng Ju Tuang Masaany Mansor Source Type: research
Letter to the Editor: "Rosai Dorfman: Rare Cause of Cervical Lymphadenopathy"
Ear Nose Throat J. 2023 Oct 16:1455613231205538. doi: 10.1177/01455613231205538. Online ahead of print.ABSTRACTWe read with great interest the article by Kobayashi KE et al. published in 2023 entitled: "Presentation of external ear Rosai-Dorfman disease with laryngeal involvement" and wish to reconnoiter Rosai-Dorfman Disease's (RDD) clinical entities and the possible implications from the perspective of otology.PMID:37843046 | DOI:10.1177/01455613231205538 (Source: Ear, Nose and Throat Journal)
Source: Ear, Nose and Throat Journal - October 16, 2023 Category: ENT & OMF Authors: Muhammad Raziin Zainal Abidin Geng Ju Tuang Masaany Mansor Source Type: research
Letter to the Editor: "Rosai Dorfman: Rare Cause of Cervical Lymphadenopathy"
Ear Nose Throat J. 2023 Oct 16:1455613231205538. doi: 10.1177/01455613231205538. Online ahead of print.ABSTRACTWe read with great interest the article by Kobayashi KE et al. published in 2023 entitled: "Presentation of external ear Rosai-Dorfman disease with laryngeal involvement" and wish to reconnoiter Rosai-Dorfman Disease's (RDD) clinical entities and the possible implications from the perspective of otology.PMID:37843046 | DOI:10.1177/01455613231205538 (Source: Ear, Nose and Throat Journal)
Source: Ear, Nose and Throat Journal - October 16, 2023 Category: ENT & OMF Authors: Muhammad Raziin Zainal Abidin Geng Ju Tuang Masaany Mansor Source Type: research
Letter to the Editor: "Rosai Dorfman: Rare Cause of Cervical Lymphadenopathy"
Ear Nose Throat J. 2023 Oct 16:1455613231205538. doi: 10.1177/01455613231205538. Online ahead of print.ABSTRACTWe read with great interest the article by Kobayashi KE et al. published in 2023 entitled: "Presentation of external ear Rosai-Dorfman disease with laryngeal involvement" and wish to reconnoiter Rosai-Dorfman Disease's (RDD) clinical entities and the possible implications from the perspective of otology.PMID:37843046 | DOI:10.1177/01455613231205538 (Source: Ear, Nose and Throat Journal)
Source: Ear, Nose and Throat Journal - October 16, 2023 Category: ENT & OMF Authors: Muhammad Raziin Zainal Abidin Geng Ju Tuang Masaany Mansor Source Type: research
Malignus eml őtumor? Gyulladásos emlőelváltozás? Ritka benignus kórkép?
CONCLUSION: Rosai-Dorfman disease confined to the breast is extremely rare, that clinically may mimic breast cancer.PMID:37747834 | DOI:10.1556/1046.2023.30003 (Source: Magyar Sebeszet)
Source: Magyar Sebeszet - September 25, 2023 Category: Surgery Authors: Edina Zita Kiss Ákos Botos Zolt án Szöllősi Erika T óth Source Type: research
Malignus eml őtumor? Gyulladásos emlőelváltozás? Ritka benignus kórkép?
CONCLUSION: Rosai-Dorfman disease confined to the breast is extremely rare, that clinically may mimic breast cancer.PMID:37747834 | DOI:10.1556/1046.2023.30003 (Source: Magyar Sebeszet)
Source: Magyar Sebeszet - September 25, 2023 Category: Surgery Authors: Edina Zita Kiss Ákos Botos Zolt án Szöllősi Erika T óth Source Type: research
