Atypical Mayer-Rokitansky-K üster-Hauser Syndrome with Bilateral Inguinal Hernia of Adnexa—Laparoscopic Transabdominal Preperitoneal Repair with Ovarian Plication
Atypical Mayer-Rokitansky-K üster-Hauser syndrome is a müllerian agenesis associated with malformations of kidneys or ovaries, including müllerian aplasia, renal aplasia, and cervicothoracic somite dysplasia [1]. Incidence of Mayer-Rokitansky-Küster-Hauser syndrome with genital inguinal hernia is rare and under-reported [2 ,3]. Nonfusion of müllerian ducts in embryonic life leads to hypermobility of ovary and ligaments predisposing to inguinal hernia [3]. Hernia repair and ovarian plication may be considered because it prevents ovarian torsion and infarction and preserves ovarian function [4]. (Source: The Journal of ...
Source: The Journal of Minimally Invasive Gynecology - April 7, 2023 Category: OBGYN Authors: Reeta Mahey, Pallavi Gupta, Rohitha Cheluvaraju, Kamal Kataria, Smita Manchanda, Monika Rajput, Neerja Bhatla Tags: Images in Gynecologic Surgery Source Type: research
Atypical MRKHS with bilateral inguinal hernia of adnexa - Laparoscopic TAPP repair with ovarian plication
Atypical Mullerian Rokitansky Kuster Hauser Syndrome (MRKHS) is mullerian agenesis associated with malformations of kidneys or ovaries, including MURCS (mullerian aplasia, renal aplasia, and cervicothoracic somite dysplasia) [1]. Incidence of MRKHS with genital inguinal hernia is rare and under-reported [2,3]. Non-fusion of Mullerian ducts in embryonic life leads to hypermobility of ovary and ligaments predisposing to inguinal hernia [3]. Hernia repair and ovarian plication may be considered as it prevents ovarian torsion, infarction and preserves ovarian function [4]. (Source: The Journal of Minimally Invasive Gynecology)
Source: The Journal of Minimally Invasive Gynecology - April 7, 2023 Category: OBGYN Authors: Reeta Mahey, Pallavi Gupta, Rohitha Cheluvaraju, Kamal Kataria, Smita Manchanda, Monika Rajput, Neerja Bhatla Tags: IMAGES IN Gynecological Surgery Source Type: research
Infrarenal Transposition of the Superior Mesenteric Artery in Wilkie ’s Syndrome
Objective: Superior mesenteric artery syndrome (SMAS), also known as Wilkie ’s syndrome, mesenteric duodenal compression syndrome, or cast syndrome, is a rare entity defined as a compression of the third portion of the duodenum between the superior mesenteric artery and abdominal aorta, due to narrowing of the space between them. This syndrome was first described by the A ustrian professor Carl Freiherr von Rokitansky in 1861 as an autopsy finding. SMAS is primarily attributed to loss of the intervening mesenteric fat pad, leading to partial or complete duodenal obstruction. (Source: EJVES Extra)
Source: EJVES Extra - April 6, 2023 Category: Surgery Authors: T. Ali, J. Tomka, I. Bakirli Source Type: research
A life course perspective on Mayer-Rokitansky-K üster-Hauser syndrome: women's experiences and negotiations of living with an underdeveloped uterus and vagina
CONCLUSION: Using the life course framework contributed to a holistic understanding of life with MRKH syndrome by showing how the meaning and consequences of the congenital condition changed over time and in adaptation to gendered and age-related social norms and expectations.IMPLICATIONS FOR REHABILITATIONThe perceived meaning and impact of living with Mayer-Rokitansky-Küster-Hauser syndrome change over time, and women's information and support needs thus change accordinglySensitive, clinical communication is essential when discussing treatment optionsOnline communities may provide support and reduce feelings of loneline...
Source: Disability and Rehabilitation - March 29, 2023 Category: Rehabilitation Authors: Amalie Hahn Jensen Morten Krogh Herlin Ida Vogel Stina Lou Source Type: research
A life course perspective on Mayer-Rokitansky-K üster-Hauser syndrome: women's experiences and negotiations of living with an underdeveloped uterus and vagina
CONCLUSION: Using the life course framework contributed to a holistic understanding of life with MRKH syndrome by showing how the meaning and consequences of the congenital condition changed over time and in adaptation to gendered and age-related social norms and expectations.IMPLICATIONS FOR REHABILITATIONThe perceived meaning and impact of living with Mayer-Rokitansky-Küster-Hauser syndrome change over time, and women's information and support needs thus change accordinglySensitive, clinical communication is essential when discussing treatment optionsOnline communities may provide support and reduce feelings of loneline...
Source: Disability and Rehabilitation - March 29, 2023 Category: Rehabilitation Authors: Amalie Hahn Jensen Morten Krogh Herlin Ida Vogel Stina Lou Source Type: research
A life course perspective on Mayer-Rokitansky-K üster-Hauser syndrome: women's experiences and negotiations of living with an underdeveloped uterus and vagina
CONCLUSION: Using the life course framework contributed to a holistic understanding of life with MRKH syndrome by showing how the meaning and consequences of the congenital condition changed over time and in adaptation to gendered and age-related social norms and expectations.IMPLICATIONS FOR REHABILITATIONThe perceived meaning and impact of living with Mayer-Rokitansky-Küster-Hauser syndrome change over time, and women's information and support needs thus change accordinglySensitive, clinical communication is essential when discussing treatment optionsOnline communities may provide support and reduce feelings of loneline...
Source: Disability and Rehabilitation - March 29, 2023 Category: Rehabilitation Authors: Amalie Hahn Jensen Morten Krogh Herlin Ida Vogel Stina Lou Source Type: research
Letter to the Editor: Sexuality After Laparoscopic-Assisted Davydov's Neovaginoplasty in Mayer-Rokitansky-K üster-Hauser Syndrome
J Obstet Gynaecol Can. 2023 Feb;45(2):112-113. doi: 10.1016/j.jogc.2022.08.019.NO ABSTRACTPMID:36925222 | DOI:10.1016/j.jogc.2022.08.019 (Source: Journal of Obstetrics and Gynaecology Canada : JOGC)
Source: Journal of Obstetrics and Gynaecology Canada : JOGC - March 16, 2023 Category: OBGYN Authors: Dubravko Habek Source Type: research
1. Surgical Correction of Vaginal Agenesis via Vecchietti Procedure
A 18-year old female presented to pediatric gynecology clinic with primary amenorrhea. She had age appropriate secondary sex characteristics (breast and pubic hair Tanner 5) and a shallow 1.5 cm vagina. Work up included Estradiol 94 pg/ml, TSH 1.34 uIU/ml, Prolactin 7.2 ng/ml, FSH 4.9 mIU/ml and LH 18.4 mIU/ml and 46 XX karyotype. Pelvic ultrasound showed rudimentary uterine horns and normal ovaries. Patient had normal kidneys and spine. Diagnosis of MRKH syndrome was made. She attempted vaginal dilation for nine months which was not successful. (Source: Journal of Pediatric and Adolescent Gynecology)
Source: Journal of Pediatric and Adolescent Gynecology - March 11, 2023 Category: OBGYN Authors: Ecem Esencan, Brad St. Martin, Oz Harmanli, Alla Vash-Margita Tags: (1) Source Type: research
35. A Patient with Rubinstein-Taybi Syndrome Found to Have M üllerian Agenesis: A Previously Unreported Presentation
Rubinstein-Taybi syndrome (RTS) is a genetic condition caused by either a mutation in the CREBBP (type 1) or EP300 (type 2) gene and is characterized by short stature, failure to thrive, gastrointestinal motility issues, characteristic facial features, intellectual disability, and variable malformations including septate uterus. M üllerian agenesis, or Mayer-Rokitansky-Küster-Hauser syndrome (MRKH), is defined as congenital aplasia of the uterus and upper vagina. Though there are several candidate genes that are associated with MRKH, a single causal genetic mutation is rarely identified. (Source: Journal of Pediatric and...
Source: Journal of Pediatric and Adolescent Gynecology - March 11, 2023 Category: OBGYN Authors: Lauryn P. Roth, Lissa X. Yu, Jodie Johnson, Brittany N. Simpson, Christine Pennesi Source Type: research
45. Mullerian Agenesis: Evaluating Ovarian Insufficiency Without the Main Vital Sign
There are no case reports of concomitant of fragile X mutation and Mayer-Rokitansky-Kuster-Hauser syndrome (MRKH). Their combination presents a novel diagnostic challenge in monitoring for the development of primary ovarian insufficiency, a known complication of Fragile X mutation. (Source: Journal of Pediatric and Adolescent Gynecology)
Source: Journal of Pediatric and Adolescent Gynecology - March 11, 2023 Category: OBGYN Authors: Melissa Parks, Ariana Hess Source Type: research
93. Use of Pelvic Floor Botox Injections to Address Myofascial Pain as a Barrier to Dilation in a Patient with Vaginal Agenesis
We present a case of botulinum toxin (Botox) injections of the pelvic floor in a patient with Mayer-Rokitansky-Kuster-Hauser syndrome (MRKH) to overcome persistent pelvic floor pain with dilation and intercourse. (Source: Journal of Pediatric and Adolescent Gynecology)
Source: Journal of Pediatric and Adolescent Gynecology - March 11, 2023 Category: OBGYN Authors: Mina M. Farahzad, Elisabeth H. Quint, Olivia K. Winfrey, Gabrielle T. Whitmore Source Type: research
91. Understanding Psychological Adjustment in Mayer-Rokitansky-K üster-Hauser Syndrome: A Systematic Review of Qualitative and Quantitative Studies
Mayer-Rokitansky-K üster-Hauser Syndrome (MRKH) is characterised by complete or partial absence of the uterus, cervix and vagina in otherwise typically developed females. Psychological and sexual distress are common in MRKH, yet evidence based psychological support is lacking in clinical practice. To understand facto rs associated with distress and inform intervention development, this review aimed to evaluate evidence of associations between psychological and sexual adjustment outcomes and clinical, demographic and potentially modifiable psychosocial factors in MRKH. (Source: Journal of Pediatric and Adolescent Gynecology)
Source: Journal of Pediatric and Adolescent Gynecology - March 11, 2023 Category: OBGYN Authors: Susan Carroll, Stephen McIntyre, Rona Moss-Morris, Marc Laufer Source Type: research
A female infant with rectovestibular fistula and imperforate hymen
Kiran Khedkar, Yashwant R Lamture, Sham Lohia, Harshal Atul TayadeJournal of Indian Association of Pediatric Surgeons 2023 28(2):177-178
In a female neonate with anorectal malformation (ARM), the diagnosis is usually simple. But when there are two openings in the introitus and absent anal opening at the normal site, the scenario poses a diagnostic challenge. Careful and detailed evaluation of anomaly is therefore necessary before planning definitive correction. Imperforate hymen, although is not commonly associated with ARM should always be kept in mind as a differential diagnosis and other vaginal anomalies like Mayer&#x...
Source: Journal of Indian Association of Pediatric Surgeons - March 3, 2023 Category: Surgery Authors: Kiran Khedkar Yashwant R Lamture Sham Lohia Harshal Atul Tayade Source Type: research
Hemi-hysterectomy for mrkh syndrome
The objective of this video is to illustrate surgical techniques and identify critical anatomic structures to complete a laparoscopic hemi-hysterectomy for a patient with Mayer-Rokitansky-K üster-Hauser (MRKH) Syndrome. (Source: American Journal of Obstetrics and Gynecology)
Source: American Journal of Obstetrics and Gynecology - March 1, 2023 Category: OBGYN Authors: A. Nimz, T. Baker, C. Ramirez, A. Truehart Tags: Videofests Source Type: research
