Pulmonary alveolar microlithiasis: A report on two familial cases in Morocco
CONCLUSION: PAM is known to be radio-clinically dissociative. In typical cases, radiology can suggest the diagnosis, which is often confirmed by SLC34A2 mutation or microliths in BAL or sputum. The prognosis is compromised in the long-term. The only effective treatment nowadays is lung transplantation.PMID:37543507 | DOI:10.1016/j.rmr.2023.06.006 (Source: Revue des Maladies Respiratoires)
Source: Revue des Maladies Respiratoires - August 5, 2023 Category: Respiratory Medicine Authors: A Tebay K Bouti S Hammi Source Type: research