Adrenal carcinoma in children: longitudinal study in minas gerais, brazil
Conclusions: Low age at diagnosis, predomina nce of cases with localized disease and complete tumor resection - with only one case of tumor capsule rupture - can possibly explain the favorable evolution of the studied population. The long period between onset of symptoms and diagnosis highlights the importance of training pediatricians for ear ly recognition of AC signs and symptoms. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Pain perception and pain coping mechanisms in children and adolescents with juvenile fibromyalgia and polyarticular juvenile idiopathic arthritis
Conclusions: Patients with JIA and JFM behave differently in relation to pain perception and the development pain coping mechanisms. Pain should be evaluated from different perspectives for an individualized and efficient treatment of patients. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Is there an association between glucocorticoid use and fractures? a comparative study in a trauma hospital
Conclusions: This study did not find an association between previous glucocorticoid use and the occurrence of fractures in children and adolescents. The age range of 10- to 14 years-old, severe trauma, and physical activity were associated with an increased risk for fractures. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Adrenal cortical carcinoma in infancy
(Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Breatfeeding and consumption of sweetened foods
RESUMO Objetivo: A s índrome de Leigh é uma doença neurodegenerativa com incidência de 1:40.000 nados-vivos. Apresenta ampla heterogeneidade clínica, bioquímica e genética, mas com alterações neuropatorradiológicas homogêneas. Não existe tratamento específico, e o prognóstico é reservado. O objetivo deste estudo foi familiarizar os profissionais de saúde com a doença. Descrição do caso: Menina de 16 meses, com hipotonia axial e atraso do desenvolvimento psicomotor. Dos exames realizados: cariótipo, potenciais auditivos evocados e avaliação oftalmológica normais; presença de hiperlactacide mia e...
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

Leigh syndrome: a case report with a mitochondrial dna mutation
RESUMO Objetivo: A s índrome de Leigh é uma doença neurodegenerativa com incidência de 1:40.000 nados-vivos. Apresenta ampla heterogeneidade clínica, bioquímica e genética, mas com alterações neuropatorradiológicas homogêneas. Não existe tratamento específico, e o prognóstico é reservado. O objetivo deste estudo foi familiarizar os profissionais de saúde com a doença. Descrição do caso: Menina de 16 meses, com hipotonia axial e atraso do desenvolvimento psicomotor. Dos exames realizados: cariótipo, potenciais auditivos evocados e avaliação oftalmológica normais; presença de hiperlactacide mia e...
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

Leukoencephalopathy with evanescent white matter: a case report
RESUMO Objetivo: Descrever uma crian ça diagnosticada com leucoencefalopatia com substância branca evanescente (LSBE), uma doença genética rara que possui padrão de herança autossômico recessivo. Descrição do caso: Criança do sexo masculino, com 5 meses de idade, que mostrava recusa da amamentação e sonolência, começou a apresentar quadro de desidratação, com boca seca, aumento da temperatura corporal e adipsia. Com o passar dos dias, os sintomas agravaram-se. O lactente apresentou-se muito sonolento e foi transferido para a unidade de tratamento intensivo (UTI), onde permaneceu por uma semana. Nesse pe...
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

Granulomatous perioral dermatitis with extra-facial involvement in childhood: good therapeutic response with oral azithromycin
RESUMO Objetivo: Apresentar um caso de dermatite perioral granulomatosa (DPG) com acometimento extrafacial e resposta terap êutica satisfatória ao uso de macrolídeo oral por curto período. Descrição do caso: Escolar de nove anos, sexo feminino, com quadro exuberante de DPG com acometimento extrafacial. Durante o período de evolução, submeteu-se a múltiplas terapêuticas ineficazes, apresentando melhora signif icativa das lesões após o uso de azitromicina por cinco dias. Comentários: A DPG é uma afecção dermatológica inflamatória representada por erupções papuloeritematosas em região perioral, nas...
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

Psychometric properties of functional capacity tests in children and adolescents: systematic review
Conclusions: Most studies investigated 6MWT measurement properties. Validity of 6MWT varied according to different pediatric populations. The use of 6MWT, ISWT and 3MST tests to measure clinically important changes in children and adolescents with cardiorespiratory diseases is still unclear. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

Socioeconomic and nutritional characteristics of children and adolescents with sickle cell anemia: a systematic review
Conclusions: Children and adolescents with sickle cell anemia have socioeconomic limitations and worse nutritional conditions, when compared to reference populations. These limitations may lead to worse growth and greater occurrence of possible complications that can impair their quality of life. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

Body dissatisfaction, physical activity, and sedentary behavior in female adolescents
Conclusions: This study concluded that female adolescents with higher cell phone time also present higher body dissatisfaction, as well as the most physically active ones. All body composition measurements were associated with body dissatisfaction, mainly body mass index, waist circumference, and waist-to-height ratio. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

Impulse oscillometry and spirometry in schoolers submitted to the six-minute walk test
Conclusions: Repercussions were: increase in central and total airway resistance and reduction of FEF25-75% after 6MWT in schoolchildren, suggesting that greater attention should be given to submaximal tests in children with predisposition to airways alterations. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

Overweight, perceived environment, and social deprivation: a study on the perception of parents or guardians
Conclusions: The perceived environment of the residential area infrastructure might be related to neighborhood social deprivation and the presence of overweight in children and adolescents. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

The use of ultrasonography to evaluate muscle thickness and subcutaneous fat in children and adolescents with cystic fibrosis
Conclusions: Patients with CF presented a reduction in subcutaneous fat content. Muscle thickness correlated with FVC and nutritional parameters. In addition, US findings correlated positively with skinfold measurements. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research

Evaluation of quality of life of parents and caregivers of asthmatic children
Conclusions: Parents/caregiversof children with asthma have a lower quality of life compared to parents/caregivers of healthy children. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - December 12, 2018 Category: Pediatrics Source Type: research