A recurrent mutation in tshb gene underlying central congenital hypothyroidism undetectable in neonatal screening
ABSTRACT Objective: To describe the case of a patient with central congenital hypothyroidism (CCH) due to a recurrent mutation in the TSHB gene, as well as to conduct a genetic study of his family. Case description: It is presented a case report of a 5-month-old boy with a delayed diagnosis of isolated CCH in whom the molecular analysis was performed 12 years later and detected a recurrent mutation (c.373delT) in TSHB gene. The parents and sister were carriers of the mutant allele. Comments: The c.373delT mutation has previously been reported in patients from Brazil, Germany, Belgium, United States, Switzerland, Argentina,...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Pre and post-operative otorhinolaryngology surgery care in patients with glycogen storage disease type 1
ABSTRACT Objective: To discuss aspects of pre and post-operative otorhinolaryngology surgery in patients with glycogen storage disease type 1b. Case description: Description of three clinical cases with probable glycogen storage disease type 1b who underwent otorhinolaryngology surgery, showing the importance of multidisciplinary interaction to avoid episodes of hypoglycemia. Comments: Patients with glycogen storage disease type 1b present recurrent infections, including the otorhinolaryngology affections. When there is an indication for surgical treatment, the caloric intake should be carefully followed in order to preven...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Rib osteomyelitis: a rare complication of varicella
ABSTRACT Objective: To report a case of varicella complicated by acute osteomyelitis in order to remind of a rare and potentially serious complication of a very common pediatric disease. Case description: A previously healthy 3-month-old female infant with 10-day history of varicella was admitted to the hospital for fever, groan and prostration. The initial laboratorial evaluation was compatible with bacterial sepsis. By the third day after admission, a swelling of the seventh left rib had developed. The ultrasound and scintigraphy evaluation suggested rib osteomyelitis. Blood cultures were negative. The patient completed ...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Adolescent patients and the clinical decision about their health
Conclusions: International guidelines recommend that adolescents participate in discussions about their illness, treatment and decision-making. However, there is no universally accepted consensus on how to assess the decision-making ability of these patients. Despite this, when possible, the adolescent should be included in a serious, honest, respectful and sincere process of deliberation.RESUMO Objetivo: Realizar uma revis ão da literatura sobre a participação do adolescente na tomada de decisão sobre a sua saúde. Fonte de dados: Revisão nos bancos Scientific Electronic Library On...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Antibiotics for appendicectomy in children and adolescents during the perioperative period: an integrative review
Conclusions: There are several clinical protocols with different antibiotics. However, there is no standardization concerning the type of antibiotic drug, time of use, or route.RESUMO Objetivo: Analisar o uso de antibi óticos em crianças e adolescentes no perioperatório de apendicectomia. Fonte de dados: Realizou-se uma revisão integrativa, nas bases de dados MEDLINE, Literatura Latino-Americana e do Caribe em Ciências da Saúde (LILACS) e Cochrane e no portal PubMed, sem limite de tempo. As palavras-chave utilizadas foram: apendicite, criança, adolescente e antibacterianos co...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Baby friendly hospital initiative: 25 years of experience in brazil
Conclusions: The BFHI has contributed to breastfeeding in Brazil in recent decades. Greater support for public policies is needed to expand the number of accredited institutions in the country.RESUMO Objetivo: Descrever a experi ência de 25 anos da Iniciativa Hospital Amigo da Criança (IHAC) no Brasil, cuja primeira unidade foi implementada em 1992. Métodos: Informações e dados foram obtidos em publicações nos sites da Organização Mundial da Saúde (OMS), do Fundo Internacional de Emergência para a Infância das Nações Unidas (UNIC...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Physicians’ knowledge about patients’ religious beliefs in pediatric care
Conclusions: Although most pediatricians and residents consider themselves able to deal with the most prevalent religions in Brazil and affirm that spirituality is beneficial during the death process, little importance is given to the spiritual identity of their patients, which could limit an appropriate approach to their death process.RESUMO Objetivo: Descrever o conhecimento dos m édicos pediatras e residentes de pediatria a respeito do significado da morte segundo as religiões mais prevalentes no Brasil. Métodos: Estudo transversal em que foi aplicado um questionário aos médicos pediat...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Analysis of the differences between the prescribed and the administered diet to preterm infants using an electronic too
Conclusions: The use of a computational routine was important to verify differences between the prescribed and the administered diet. This analysis is necessary to minimize calcul ation errors and to speed up health providers ’ decisions about the nutritional approach, which can contribute to patients ’ safety and to good nutritional practice. Very low birth weight infants are extremely vulnerable to nutritional deficiencies and any reduction in macronutrients they receive may be harmful to achieve satisfactory growth.RESUMO Objetivo: Elaborar um instrumento eletr ônico para análise da adequa&ccedi...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

X-linked adrenoleukodystrophy in brazil: a case series
Conclusions: All phenotypes of X-linked adrenoleukodystrophy, except for myelopathy in women, were presented in the studied population, which mainly consisted of children and adolescents. Prevalent signs and symptoms registered in the literature were observed. Most of the patients with cerebral demyelinating inflammatory adrenoleukodystrophy were not diagnosed in time for hematopoietic stem cell transplantation.RESUMO Objetivo: Descrever pacientes com diferentes formas de adrenoleucodistrofia ligada ao X: pr é-sintomática, adrenoleucodistrofia inflamatória desmielinizante cerebral, adrenomieloneuropati...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Educational program for the promotion of knowledge, attitudes and preventive practices for children in relation to traffic accidents: experimental study
Conclusions: The educational intervention increased the level of knowledge and maintained the preventive attitudes and practices on traffic accidents at the same level in 3rd-5th grade students.RESUMO Objetivo: Avaliar o conhecimento, as atitudes e as pr áticas preventivas de acidentes de trânsito entre crianças escolares antes e depois da aplicação de um programa educativo. Métodos: Estudo experimental, com abordagens descritiva e analítica, realizado em duas escolas públicas do nordeste brasileiro. A amostra foi composta de 173 crianças do 3º ao 5º a...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Proposal and test-retest reliability of a scale for cervical, thoracic, and lumbar spine pain in brazilian young people
Conclusions: This instrument was shown to be a reliable manner to verify the pain in different regions of the spine in Brazilian young people.RESUMO Objetivo: Propor e analisar a reprodutibilidade de um instrumento para verificar a presen ça e a intensidade da dor na coluna cervical, torácica e lombar em jovens brasileiros. Métodos: Estudo de reprodutibilidade com uma amostra de 458 participantes (13 a 20 anos). Dois grupos foram formados para cada sexo de acordo com o intervalo de dias entre teste e reteste (10±3 e 28±2 dias) . Para a análise da dor na coluna, foi apresentada a fi...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Exergames in adolescents: associated factors and possible reduction in sedentary time
ABSTRACT Objective: To describe the use of exergames, associated factors and to quantify the time attributed to the use of exergames within the time spent on video games in a sample of adolescents from Curitiba, Paran á, Brazil. Methods: This was a cross-sectional study that evaluated frequency and weekly volume of physical activities using the Physical Activity Questionnaire for Adolescents. Weekly frequency and daily time of use of exergames and videogames were self-reported. Mann-Whitney and Kruskal Wallis tests were used to compare the time spent playing exergames, and Poisson regression was used to test the associations (p
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Prevalence of hepatic steatosis among children and adolescents with cystic fibrosis and its association with nutritional status
Conclusions: The frequency of HS in patients with CF is high and it is not related to malnutrition, according to the parameters of BMI, TSF and MAMC. The values of MAC and MAMC indicated a greater reserve of muscle mass in patients with HS.RESUMO Objetivo: Determinar a preval ência de esteatose hepática (EH) em crianças e adolescentes com fibrose cística (FC) e associá-la com o estado nutricional. Métodos: Estudo transversal com crianças e adolescentes com diagnóstico de FC. Foram aferidos o peso e a altura para o cálculo do índice de massa corpóre...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Intima-media thickness of the carotid arteries is affected by pubertal maturation in healthy adolescents
ABSTRACT Objective: To contribute to the assessment of normal parameters of carotid intima-media thickness (CIMT) in healthy adolescents. Methods: A cross-sectional study was conducted through clinical, laboratory and ultrasound evaluation in 61 healthy adolescents. The inclusion criteria consisted of being in good health. The exclusion criteria were: presence or history of any chronic disease; being obese or overweight according to the World Health Organization (WHO) established criterion; continuous use of medication; or presenting a febrile condition or requiring medication within 48-hours prior to assessment. The puber...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Adolescent gluten intake: population-based study in a brazilian city
ABSTRACT Objective: To estimate the prevalence of gluten intake according to demographic, socioeconomic, and health-related behavioral variables in adolescents. Methods: This is a population-based cross-sectional study with a two-stage cluster sampling, conducted in Campinas, S ão Paulo, in 2008-2009. Foods containing gluten were identified using a 24-hour Recall. We calculated the prevalence and adjusted prevalence ratios with multiple Poisson regression. Results: The study had a sample of 924 adolescents aged 10 to 19 years. Among the foods assessed, 26.9% (confidence interval of 95% - 95%CI 25.3-28.6) contained g...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Body mass index and albumin levels are associated with pulmonary function parameters in pediatric subjects with cystic fibrosis
ABSTRACT Objective: To evaluate the association of body mass index (BMI) and albumin with pulmonary function in cystic fibrosis (CF) pediatric subjects. Methods: This is a cross-sectional study with clinically stable CF ’ s subjects. Clinical (pulmonary function) and nutritional evaluation (body mass index and albumin) were performed. Univariate analysis was performed using simple linear correlations. Regression analysis was performed using an exit level of p
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Factors associated with asthma in brazilian adolescents: national adolescent school-based health survey (pense-2012)
ABSTRACT Objective: To identify factors associated with asthma in Brazilian adolescents. Methods: Cross-sectional study based on data from the 2012 National Adolescent School-based Health Survey (PeNSE), a Brazilian survey applied by a self-reported questionnaire in a representative sample of 9th-grade students. Descriptive and inferential analysis was made based on the demographic, socioeconomic, clinical, food consumption and environmental characteristics potentially associated with asthma. Adolescents who presented wheezing in the last 12 months were considered asthmatic. A multiple logistic regression model was adjuste...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Autism spectrum disorder and postnatal factors: a case-control study in brazil
Conclusions: The findings of the present study suggest that malformation, neonatal jaundice, absence of crying at birth and seizure episodes in childhood are important factors to be considered when studying the etiology of ASD.RESUMO Objetivo: Estimar, em uma popula ção brasileira, a magnitude da associação entre o transtorno do espectro do autismo (TEA) e os fatores pós-natais. Métodos: Estudo de caso controle realizado com 253 indivíduos com diagnóstico do TEA e 886 sem sinais do transtorno. Foi aplicado um questionário semiestruturado e adotou-se o modelo de...
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

Risk factors for asthma: the contribution of the brazilian national research on health of schoolchildren
(Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - October 11, 2019 Category: Pediatrics Source Type: research

ERRATUM: Breatfeeding and consumption of sweetened foods
We present the case of a 31-week preterm newborn with multiple skin lesions whose clinical, histological and immunohistochemical findings allowed the diagnosis of juvenile xanthogranuloma. Currently, the patient has nine months-old, and there is no aggravation of the skin lesions or evidence of extra-cutaneous involvement, particularly ophthalmic. Comments: Juvenile xanthogranuloma is a rare and benign condition, included in the vast group of non-Langerhans histiocytosis. It typically occurs in the pediatric age and may have a neonatal presentation. It affects predominantly the skin, in the form of papules or yellow and/or...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Juvenile xanthogranuloma: a case report
We present the case of a 31-week preterm newborn with multiple skin lesions whose clinical, histological and immunohistochemical findings allowed the diagnosis of juvenile xanthogranuloma. Currently, the patient has nine months-old, and there is no aggravation of the skin lesions or evidence of extra-cutaneous involvement, particularly ophthalmic. Comments: Juvenile xanthogranuloma is a rare and benign condition, included in the vast group of non-Langerhans histiocytosis. It typically occurs in the pediatric age and may have a neonatal presentation. It affects predominantly the skin, in the form of papules or yellow and/or...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Precordial pain, leukocytosis and bicytopenia in a teenager with systemic juvenile idiopathic arthritis under immunosuppressive therapy
ABSTRACT Objective: To highlight the importance of the new classification criteria for the macrophage activation syndrome (MAS) in systemic juvenile idiopathic arthritis in order to reduce morbidity and mortality outcome related to this disease. Case description: A 12-year-old female patient with diagnosis of systemic juvenile idiopathic arthritis under immunosuppression therapy for two years developed cough, acute precordial chest pain, tachypnea, tachycardia and hypoxemia for two days. Chest tomography showed bilateral laminar pleural effusion with bibasilar consolidation. The electrocardiogram was consistent with acute ...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Predictive equations of maximum oxygen consumption by shuttle run test in children and adolescents: a systematic review
Conclusions: Matsuzaka ’ s equation presented satisfactory parameters for estimates of VO2peak in children and adolescents. Although not explored in equations, body adiposity and pubertal stage are significantly associated with cardiorespiratory fitness in children and adolescents.RESUMO Objetivo: Revisar sistematicamente na literatura o n ível de evidência das equações preditivas do pico de consumo de oxigênio (VO2pico) por meio do teste de shuttle run de 20 metros (SR-20m) em crianças e adolescentes. Fonte de dados: As buscas foram conduzidas nas bases de dados eletrôni...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Exercise capacity in children and adolescents with post-infectious bronchiolitis obliterans: a systematic review
Conclusions: Findings of the study demonstrate that children and adolescents with post-infectious bronchiolitis obliterans have reduced exercise capacity.RESUMO Objetivo: Avaliar a capacidade de exerc ício em crianças e adolescentes com bronquiolite obliterante pós-infeciosa. Fonte de dados: Trata-se de uma revisão sistemática por meio das bases de dados PubMed, Literatura Latino-Americana e do Caribe em Ciências da Saúde (LILACS), Scientific Electronic Library Online (SciELO) e Physioth erapy Evidence Database (PEDro). Utilizou-se a seguinte estratégia de busca: &ldqu...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Photogrammetry: a proposal of objective assessment of chest wall in adolescent idiopathic scoliosis
Conclusions: The photogrammetry method was able to detect chest wall changes in AIS patients, besides presenting correlation between Cobb angles and lung function.RESUMO Objetivo: Avaliar o formato da caixa tor ácica em pacientes com escoliose idiopática do adolescente (EIA), comparando-os com indivíduos saudáveis e analisar a associação do formato da caixa torácica com a deformidade da coluna vertebral e função pulmonar em pacientes com EIA. Métodos: Estudo transversal que avaliou 30 pacientes com EIA e 20 indivíduos saudáveis com idade en...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Risk behavior for bulimia among adolescents
ABSTRACT Objective: To analyze the risk behavior for bulimia among female adolescents from public and private high schools. Methods: A cross-sectional study with a random sample of 850 female students aged 15-18 years was carried out in a city in northeastern Brazil, using the Bulimic Investigatory Test of Edinburgh (BITE) to assess the risk behavior for bulimia. Data were analyzed using the Statistical Package for the Social Sciences (SPSS) software and the Pearson ’ s chi-square , Fisher ’ s exact and robust Poisson regression tests, adopting the significance level of 5%. Results: Less than half of the sample...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Subjective sleep need and daytime sleepiness in adolescents
ABSTRACT Objective: To analyze the contribution of subjective sleep need for daytime sleepiness in adolescents, and to compare questions about sleep, age and body mass index between adolescents who considered to sleep enough and those who reported the need for more sleep. Methods: This is a descriptive, epidemiological and cross-sectional study. Data collection was performed in August 2016, with 773 adolescents aged 14-19 years old, from Paranagu á, Paraná, Southern Brazil. The analysis included the following variables: time in bed, half-sleep phase, sleep need, social jetlag, daytime sleepiness, body mass in...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Association of flexibility with sociodemographic factors, physical activity, muscle strength, and aerobic fitness in adolescents from southern brazil
Conclusions: Lower levels of flexibility were associated with male adolescents and with reduced strength levels.RESMO Objetivo: Identificar os fatores sociodemogr áficos, de atividade física e da aptidão física associados à flexibilidade. Métodos: Estudo transversal com 909 adolescentes (486 meninas) de 14 a 19 anos da cidade de São José, Santa Catarina, Brasil. A flexibilidade foi avaliada por meio do teste de sentar e alcançar. Os dados sociodemo gráficos e de atividade física foram levantados por meio de questionário autoadministrado. A ...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Impact of physical activity correlates in the isolated and combined presence of insufficient level of physical activity and high screen time among adolescents
Conclusions: Physical activity correlates can have an impact on the insufficient level of physical activity and high screen time, especially among girls.RESUMO Objetivo: Identificar o impacto dos correlatos da atividade f ísica (AF) com a presença isolada e a combinada da prática insuficiente de AFs e do elevado tempo de tela em adolescentes. Métodos: Estudo transversal, representativo, com amostra de 786 adolescentes (16,2±1,1 anos; 53,9% de meninas) selecionados aleatoriamente nas escolas de São José dos P inhais, PR. Foram analisados: sexo, estado nutricional, classe econ...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Physical activity level in asthmatic adolescents: cross-sectional population-based study
Conclusions: Adolescents diagnosed with asthma were more physically active than their non-asthmatic peers.RESUMO Objetivo: Avaliar o n ível de atividade física (AF) em asmáticos, comparando com não asmáticos, em estudo populacional. Métodos: Estudo transversal com adolescentes de 13 a 14 anos que participaram do estudo International Study of Asthma and Allergies in Childhood (ISAAC). Os indivíduos foram classificados em tr ês grupos: indivíduos com asma ativa, indivíduos com diagnóstico de asma e assintomáticos respiratórios. Para ava...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Cardiometabolic risk factors associated with active commuting to school
Conclusions: The prevalence of active commuting in the sample studied is low and it was shown to have a crude association with glucose and LDL cholesterol levels in students. However, sociodemographic factors seem to influence these associations.RESUMO Objetivo: Verificar se existe associa ção entre fatores de risco cardiometabólicos e deslocamento ativo à escola em crianças e adolescentes. Métodos: Foram avaliados 1.743 escolares, de sete a 17 anos, do município de Santa Cruz do Sul (RS). A forma de deslocamento até a escola foi investigada por meio de question&aacut...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Consumption of minimally processed and ultra-processed foods among students from public and private schools
Conclusions: Foods from G1 represent the highest percentage of total energy intake, while those from G4 const itute a third of calories consumed. Processed juice, sandwich cookie, processed cake, and breakfast cereals are more frequent among private school students; snacks and juice powder are more common for students from public schools.RESUMO Objetivo: Comparar e analisar o consumo de alimentos minimamente processados e ultraprocessados entre escolares das redes p ública e privada. Métodos: Estudo realizado em Uberlândia, MG, com escolares do quinto ano do ensino fundamental em nove escolas (trê...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Different response to exposure to air pollutants in girls and boys
Conclusions: Significant effect in daily hospitalizations due to respiratory diseases related to exposure to fine particulate matter was noted for girls, suggesting the need for stratification by sex in further stu dies.RESUMO Objetivo: Identificar associa ção entre exposição ao material particulado fino e internações por doenças respiratórias em crianças de até dez anos de idade, no município de Cuiabá, MT, estratificando a análise por sexo e calculando excesso de custos. Métodos: Estudo ecológico de séries temp...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Impact of the appendiceal position on the diagnosis and treatment of pediatric appendicitis
ABSTRACT Objective: To investigate how symptoms vary according to the appendiceal position in pediatric patients and to demonstrate that the laparoscopic approach is safe and effective in any appendiceal location by comparing each location to another. Methods: The medical records of 1,736 children aged 14 or younger who underwent laparoscopic appendectomy over a period of 14 years were analyzed retrospectively. Patients were divided according to the position of the appendiceal tip into four groups: anterior, pelvic, retrocecal and subhepatic. The Kruskal-Wallis and chi-square tests were used with the Bonferroni correction,...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Invasive non-type b haemophilus influenzae disease: report of eight cases
ASTRACT Objective: To describe eight cases of invasive non-type b Haemophilus influenzae disease in children admitted to Hospital de Cl ínicas of Universidade Estadual de Campinas. Cases description: In 2015, there were eight cases of invasive non-type b H. influenzae disease. We tested the ampicillin sensitivity and beta-lactamase production of the strains identified and performed the genotyping. Molecular typing was determined by Pulsed-Field Gel Electrophoresis. Four patients were diagnosed with bacteremia; in two cases, H. influenzae was detected in the pleural fluid, and two patients had meningitis. Patients wi...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Early detection of poor adherence to treatment of pediatric rheumatic diseases: pediatric rheumatology adherence questionnaire - a pilot study
Conclusions: The usefulness of this questionnaire in clinical practice should be still evaluated. Due to the importance of a tool for the early detection of rheumatic patients at risk of poor adherence to treatment, the new PRAQ questionnaire should be reviewed and applied in a larger study to better define its validity and reliability.RESUMO Objetivo: Desenvolver um question ário que permitisse a detecção precoce de pacientes em risco de má adesão ao tratamento medicamentoso e não medicamentoso para crianças e adolescentes com doenças reumáticas crônicas...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Perinatal care in a northeastern brazilian state: structure, work processes, and evaluation of the components of essential newborn care
Conclusions: The distribution of NICU beds between capital city and other cities of the State is adequate, considering Brazilian guidelines. However, there was a low adherence to the protocols for hypertensive and hemorrhagic emergencies, and a low coverage of humanization policies, pregnancy risk classification and ENC practices, especially breastfeeding in the first hour of life, and companion always during birth.RESUMO Objetivo: Descrever a estrutura e os processos de atendimento a gestante/rec ém-nascido, incluindo os componentes do Essential Newborn Care (ENC), das maternidades de Sergipe, Brasil. Método...
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

Poor adherence to drug treatment in children and adolescents with autoimmune rheumatic diseases
(Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - July 23, 2019 Category: Pediatrics Source Type: research

ADVERSE REACTION TO ANESTHESIA IN A M.8993T>C CARRIER WITH LEIGH SYNDROME
RESUMO Objetivo: Relatar um caso de p ênfigo neonatal em paciente que manifestou lesões cutâneas extensas e críticas ao nascimento. Descrição do caso: Recém-nascido do sexo masculino com lesões vesicobolhosas extensas em região anterior do tórax e abdome, desde o nascimento. Admitido na ala pediátrica de um hospital para di agnóstico etiológico e tratamento. Com base na história materna e na avaliação clínica, concluiu tratar-se de pênfigo vulgar neonatal. O paciente apresentou evolução s...
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Neonatal pemphigus in an infant born to a mother with pemphigus vulgaris: a case report
RESUMO Objetivo: Relatar um caso de p ênfigo neonatal em paciente que manifestou lesões cutâneas extensas e críticas ao nascimento. Descrição do caso: Recém-nascido do sexo masculino com lesões vesicobolhosas extensas em região anterior do tórax e abdome, desde o nascimento. Admitido na ala pediátrica de um hospital para di agnóstico etiológico e tratamento. Com base na história materna e na avaliação clínica, concluiu tratar-se de pênfigo vulgar neonatal. O paciente apresentou evolução s...
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Association of meningitis and pericarditis in invasive pneumococcal disease: a rare case
This report describes the unfavorable clinical course of a previously healthy 6-months-old female infant who initially presented symptoms of fever and respiratory problems. A chest X-ray revealed an increased cardiac area with no radiographic changes in the lungs. After identifying a pericardial effusion, the patient experienced seizures and went into coma. Pneumonia was excluded as a possibility during the clinical investigation. However, Streptococcus pneumoniae was identified in the cerebrospinal fluid and blood cultures. An initial neurological examination showed that the patient was brain dead, which was then later co...
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Occasional digestive hemorrhage in children due to strongyloidiasis: importance of parasitologic testing
RESUMO Objetivo: Descrever um caso incomum de infec ção por Strongyloides stercoralis (S. stercoralis) em paciente de quatro meses de idade e ressaltar a importância do diagnóstico precoce. Descrição do caso: Paciente masculino, procedente e residente de Videira, Santa Catarina, Brasil, nasceu pré-termo, parto cesárea, peso de nascimento 1. 655 g, e permaneceu na Unidade de Terapia Intensiva neonatal e intermediária por 20 dias. Aos quatro meses de idade, começou a evacuar fezes sanguinolentas e foi feita hipótese de alergia à proteín...
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Effectiveness of obesity intervention programs based on guidelines for adolescent students: systematic review
Conclusions: Interventions based on physical activity and/or nutrition counseling were efficient and showed superior results in studies that associated the practice of physical activity with counseling. However, the need for new studies on educational interventions among schoolchildren and adolescents was made evident. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Should pediatricians investigate the symptoms of obsessive-compulsive disorder in children with feeding difficulties?
Conclusions: Obsessive-compulsive disorder and feeding difficulties patients share common symptoms. The present study alerts health professionals who follow patients with feeding difficulties as to the importance of investigating possible psychiatric comorbidities. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Sensory changes in mouth breathers: systematic review based on the prisma method
Conclusions: Most studies presents the occurrence of changes in sensory systems in mouth breathing children. However, sensory reception is a matter of more concern. Besides, the evaluation of sensory systems was not standardized, which may have led to less precise results in the studied population. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Evaluation of usability of a neonatal health information system according to the user’s perception
Conclusion: The level of satisfaction of the computerized health system user was considered good. No demographic factors were associated with the satisfaction of the users.RESUMO Objetivo: Mensurar o grau de satisfa ção de profissionais de saúde quanto à usabilidade de um sistema de informação em saúde neonatal e identificar os fatores que podem influenciar na satisfação do usuário frente à usabilidade. Métodos: Estudo transversal e exploratório realizado com 50 profissionais de saúde integrante s dos centros da Rede Brasileir...
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Congenital hypothyroidism as a risk factor for central hearing process disorders
Conclusions: The data obtained show a high frequency of lag symptoms in cognitive functions related to central auditory processing, particularly with regard to auditory attention, figure-background ability and auditory memory in patients with congenital hypothyroidism. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Cardiorespiratory fitness associated to teenagers’ fat: vo2max cutoff point
This study was carried out with 979 subjects aged 10 to 18.8 years, 556 (56.8%) girls. The 20 m shuttle run protocol determined the VO2max, which was analyzed in quintiles and in a numeric scale. Cutaneous fold equations determined the %BF, later classified as risk to health/obesity when>25 in girls and>20 in boys. Regression method was used - Odds Ratio (OR) and Receiver Operating Characteristics Curve (ROC curve) with α
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Functional capacity in children and adolescents with congenital heart disease
Conclusions: Children and adolescents with congenital heart disease have low functional capacity, but they are not completely sedentary.RESUMO Objetivo: Avaliar o n ível de atividade física e a capacidade funcional de crianças e adolescentes com cardiopatia congênita, além de descrever correlações entre funcionalidade, achados cirúrgicos e ecocardiográficos, perfil metabólico e inflamatório e diferenças entre cardiopatias congênitas acianótica e c ianótica. Métodos: Estudo transversal com crianças e adolesce...
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research

Evaluation of nutritional status in patients with cystic fibrosis according to age group
Conclusions: Most of the patients presented adequate nutritional status and adequate consumption of calories and macronutrients, indicating appropriate nutritional management. New studies focusing on pre school children should be performed to assess if it is possible to reduce the nutritional risk of patients with cystic fibrosis at older ages. (Source: Revista Paulista de Pediatria)
Source: Revista Paulista de Pediatria - February 5, 2019 Category: Pediatrics Source Type: research