IqYmune ® is an effective maintenance treatment for multifocal motor neuropathy: a randomised, double‐blind, multicenter cross‐over non‐inferiority study versus Kiovig® ‐ The LIME Study
Intravenous immunoglobulin (IVIg) is the gold ‐standard for maintenance treatment of multifocal motor neuropathy (MMN). This phase III, randomised, double‐blind, multicentre, active‐control, crossover study, aimed to evaluate the non‐inferiority of IqYmune® relative to Kiovig®, primarily based on efficacy criteria.Twenty ‐two adult MMN patients, treated with any brand of IVIg (except Kiovig® or IqYmune®) at a stable maintenance dose within the range of 1 to 2 g/kg every 4 to 8 weeks, were randomised to receive either Kiovig followed by IqYmune, or IqYmune followed by Kiovig. Each product was admin...
Source: Journal of the Peripheral Nervous System - November 19, 2018 Category: Neurology Authors: JM. L éger, O. Alfa‐Cissé, D. Cocito, JM Grouin, H. Katifi, E. Nobile‐Orazio, R. Ouaja, J. Pouget, YA. Rajabally, T. Sevilla, I. Merkies Tags: RESEARCH REPORT Source Type: research

2018 Peripheral Nerve Society Annual Meeting 21 ‐25 July, 2018 Baltimore, Maryland
Journal of the Peripheral Nervous System, Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - November 16, 2018 Category: Neurology Tags: PROCEEDING Source Type: research

Increased incidence of axonal Guillain ‐Barré syndrome in La Spezia area of Italy: a thirteen‐years follow‐up study
BackgroundGuillain ‐Barré syndrome (GBS) is an acute immune‐mediated polyradiculoneuropathy with a worldwide incidence of 0,81‐ 1,89 per 100,000 person‐years. In Europe and North America only 5% of patients with GBS have axonal subtypes, which in South America and Asia account for 30‐47% of cases.ObjectiveTo assess the annual incidence and clinical features of GBS in La Spezia area in Italy.Material and methodsA retrospective (from January 1st 2003 to December 31st 2011) followed by a prospective (from January 1st 2012 to December 31st 2015) analysis was carried out on patients admitted to La Spezia hospit...
Source: Journal of the Peripheral Nervous System - November 13, 2018 Category: Neurology Authors: Luana Benedetti, Chiara Briani, Alessandro Beronio, Federico Massa, Elisa Giorli, Cinzia Sani, Paola Delia, Stefania Artioli, Maria P. Sormani, Antonio Mannironi, Antonio Tartaglione, Giovanni L. Mancardi Tags: RESEARCH REPORT Source Type: research

Novel GARS mutation presenting as autosomal dominant intermediate Charcot ‐Marie‐Tooth disease
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - November 5, 2018 Category: Neurology Authors: Haitian Nan, Ryusuke Takaki, Takanori Hata, Yuta Ichinose, Mai Tsuchiya, Kishin Koh, Yoshihisa Takiyama Source Type: research

Nociceptin/orphanin FQ opioid peptide ‐receptor expression in pachyonychia congenita
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - October 17, 2018 Category: Neurology Authors: Baohan Pan, Wolfgang Schr öder, Ruth Jostock, Mary Schwartz, Gedge Rosson, Michael Polydefkis Source Type: research

Nociceptin/orphanin FQ opioid peptide receptor expression in pachyonychia congenita
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - September 26, 2018 Category: Neurology Authors: Baohan Pan, Wolfgang Schr öder, Ruth Jostock, Mary Schwartz, Gedge Rosson, Michael Polydefkis Source Type: research

Issue Information
Journal of the Peripheral Nervous System,Volume 23, Issue 3, Page 151-153, September 2018. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - September 12, 2018 Category: Neurology Source Type: research

Rituximab in chronic inflammatory demyelinating polyradiculoneuropathy with associated diseases
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - September 11, 2018 Category: Neurology Authors: Thomas Roux , Rabab Debs , Thierry Maisonobe , Timoth ée Lenglet , Cécile Delorme , Céline Louapre , Véronique Leblond , Karine Viala Source Type: research

Mandating nerve biopsy: A step towards personalizing therapy in pure neuritic leprosy
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - August 28, 2018 Category: Neurology Authors: Dinkar Kulshreshtha , Kiran Preet Malhotra , Hardeep Singh Malhotra , Anup Kumar Thacker , Ravindra Kumar Garg , Ajai Kumar Singh , Pradeep Kumar Maurya Source Type: research

Second IVIg Course in Guillain ‐Barré Syndrome patients with poor prognosis (SID‐GBS trial): protocol for a double‐blind randomized, placebo‐controlled clinical trial
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - August 27, 2018 Category: Neurology Authors: Christa Walgaard , Bart C. Jacobs , Hester F. Lingsma , Ewout W. Steyerberg , David R. Cornblath , Pieter A. van Doorn , , P.A. van Doorn , B.C. Jacobs , C. Walgaard , M.C.Y. de Wit , E.W. Steyerberg , D.R. Source Type: research

The 2016 Singapore Zika virus outbreak did not cause a surge in Guillain ‐Barré syndrome
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - August 22, 2018 Category: Neurology Authors: Thirugnanam Umapathi , Yiu ‐Wing Kam , O. Ohnmar , Brandon C. J. Ng , Yixiang Ng , M. Premikha , Yee‐Sin Leo , Lisa F. P. Ng Source Type: research

Clinical relevance of serum antibodies to GD1b in immune ‐mediated neuropathies
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - August 13, 2018 Category: Neurology Authors: Noor E. Taams , Nicolette C. Notermans , Willem ‐Jan R. Fokkink , Anne P. Tio‐Gillen , Ruth Huizinga , Marco W.J. Schreurs , Bart C. Jacobs Source Type: research

The 2016 Singapore ZIKV outbreak did not cause a surge in Guillain ‐Barré syndrome
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - August 2, 2018 Category: Neurology Authors: Thirugnanam Umapathi , Yiu ‐Wing Kam , O Ohnmar , Brandon C.J. Ng , Yixiang Ng , M Premikha , Yee‐Sin Leo , Lisa F.P. Ng Source Type: research

Mandating nerve biopsy ‐ a step towards personalizing therapy in pure neuritic leprosy
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - August 2, 2018 Category: Neurology Authors: Dinkar Kulshreshtha DM , Kiran Preet Malhotra MD , Hardeep Singh xMalhotra DM , Anup Kumar Thacker DM , Ravindra Kumar Garg DM , Ajai Kumar Singh DM , Pradeep Kumar Maurya DM Source Type: research

Serum and cerebrospinal neurofilament light chain levels in patients with acquired peripheral neuropathies
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - July 25, 2018 Category: Neurology Authors: Sara Mariotto , Alessia Farinazzo , Roberta Magliozzi , Daniela Alberti , Salvatore Monaco , Sergio Ferrari Source Type: research

Conventional and unconventional therapies in typical and atypical chronic inflammatory demyelinating polyneuropathy (CIDP) with different clinical course of progression
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - July 20, 2018 Category: Neurology Authors: Stefanie Kar Yan Hung , Fu Liong Hiew , Shanthi Viswanathan , Santhi Puvanarajah Source Type: research

Employment status of patients with chronic inflammatory demyelinating polyradiculoneuropathy
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - July 12, 2018 Category: Neurology Authors: Bogdan Bjelica , Ivana Basta , Ivo Bozovic , Aleksandra Kacar , Ana Nikolic , Aleksandra Dominovic ‐Kovacevic , Zoran Vukojevic , Vesna Martic , Aleksandar Stojanov , Gordana Djordjevic , Milutin Petrovic , Mi Source Type: research

A novel SCN9A splicing mutation in a compound heterozygous girl with congenital insensitivity to pain, hyposmia and hypogeusia
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - July 6, 2018 Category: Neurology Authors: Margherita Marchi , Vincenzo Provitera , Maria Nolano , Marcello Romano , Simona Maccora , Ilaria D'Amato , Erika Salvi , Monique Gerrits , Lucio Santoro , Giuseppe Lauria Source Type: research

Serum and CSF neurofilament light chain levels in patients with acquired peripheral neuropathies
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - July 5, 2018 Category: Neurology Authors: Sara Mariotto , Alessia Farinazzo , Roberta Magliozzi , Daniela Alberti , Salvatore Monaco , Sergio Ferrari Source Type: research

Differences between acute ‐onset chronic inflammatory demyelinating polyneuropathy and acute inflammatory demyelinating polyneuropathy in adult patients
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - June 25, 2018 Category: Neurology Authors: Lucas Alessandro , Jos é M. Pastor Rueda , Miguel Wilken , Luis Querol , Mariano Marrodán , Julián N. Acosta , Alberto Rivero , Fabio Barroso , Mauricio F. Farez Source Type: research

A unified model of the excitability of mouse sensory and motor axons
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - June 19, 2018 Category: Neurology Authors: Preet G.S. Makker , Jos é Manuel Matamala , Susanna B Park , Justin G. Lees , Matthew C Kiernan , David Burke , Gila Moalem‐Taylor , James Howells Source Type: research

Issue Information
Journal of the Peripheral Nervous System,Volume 23, Issue 2, Page 73-75, June 2018. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - June 15, 2018 Category: Neurology Source Type: research

Clinical and genetic investigation in Chinese patients with demyelinating Charcot ‐Marie‐Tooth disease
Journal of the Peripheral Nervous System,Volume 0, Issue ja, -Not available-. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - June 13, 2018 Category: Neurology Authors: Jin He , Lingling Guo , Guorong Xu , Liuqing Xu , Shan Lin , Wanjin Chen , Ning Wang Source Type: research

Robert R. Myers: In Memoriam (April 15, 1946 —April 19, 2018)
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - May 25, 2018 Category: Neurology Authors: Veronica I. Shubayev , Douglas W. Zochodne Source Type: research

Risk factors for the development of paclitaxel ‐induced neuropathy in breast cancer patients
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - May 11, 2018 Category: Neurology Authors: Jetter Robertson , Jeffrey Raizer , James S. Hodges , William Gradishar , Jeffrey A. Allen Source Type: research

Whole ‐exome sequencing reveals a novel missense mutation in the MARS gene related to a rare Charcot‐Marie‐Tooth neuropathy type 2U
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - May 9, 2018 Category: Neurology Authors: Lena Sagi ‐Dain , Lilach Shemer , Nathanel Zelnik , Yusri Zoabi , Sadeh Orit , Vardit Adir , Aharon Schif , Amir Peleg Source Type: research

Peripheral neuropathy in Tangier disease: A literature review and assessment
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - May 8, 2018 Category: Neurology Authors: Metin Mercan , Vildan Yayla , Serdar Altinay , Serhat Seyhan Source Type: research

Testing overwork weakness in Charcot ‐Marie‐tooth disease: Is it true or false?
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - May 7, 2018 Category: Neurology Authors: Valeria Prada , Laura Mori , Susanna Accogli , Matteo Rivarola , Sara Schizzi , Mernhaz Hamedani , Angelo Schenone Source Type: research

Clinical spectrum and quality of life in patients with chronic polyneuropathy: A cross ‐sectional study
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - May 7, 2018 Category: Neurology Authors: MS Panduranga , Deepti Vibha , Kameshwar Prasad , Achal Kumar Srivastava , Garima Shukla Source Type: research

A randomised, multi ‐centre phase III study of 3 different doses of intravenous immunoglobulin 10% in patients with chronic inflammatory demyelinating polyradiculoneuropathy (ProCID trial): Study design and protocol
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - April 26, 2018 Category: Neurology Authors: David R. Cornblath , Hans ‐Peter Hartung , Hans D. Katzberg , Ingemar S. J. Merkies , Pieter A. van Doorn Source Type: research

Intravenous immunoglobulin for maintenance treatment of multifocal motor neuropathy: A multi ‐center, open‐label, 52‐week phase 3 trial
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - April 25, 2018 Category: Neurology Authors: Satoshi Kuwabara , Sonoko Misawa , Masahiro Mori , Yuta Iwai , Kazuhide Ochi , Hidekazu Suzuki , Hiroyuki Nodera , Akira Tamaoka , Masahiro Iijima , Tatsushi Toda , Hiroo Yoshikawa , Takashi Kanda , Ko Saka Source Type: research

Individualized immunoglobulin therapy in chronic immune ‐mediated peripheral neuropathies*
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - April 19, 2018 Category: Neurology Authors: Jeffrey A. Allen , Melvin Berger , Luis Querol , Krista Kuitwaard , Robert D. Hadden Source Type: research

Issue Information ‐ Editorial Board
Journal of the Peripheral Nervous System,Volume 23, Issue S1, Page S1-S1, April 2018. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - April 18, 2018 Category: Neurology Source Type: research

Abstracts
Journal of the Peripheral Nervous System,Volume 23, Issue S1, Page S3-S48, April 2018. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - April 18, 2018 Category: Neurology Source Type: research

Meeting Abstracts, Proceedings
Journal of the Peripheral Nervous System,Volume 23, Issue S1, Page S2-S2, April 2018. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - April 18, 2018 Category: Neurology Source Type: research

Clinical and genetic diversities of Charcot –Marie–Tooth disease with MFN2 mutations in a large case study
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - April 11, 2018 Category: Neurology Source Type: research

The genetic heterogeneity of hereditary transthyretin amyloidosis in a sample of the Brazilian population
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - April 10, 2018 Category: Neurology Authors: Carolina Lavigne ‐Moreira , Vanessa D. Marques , Marcus V. M. Gonçalves , Mauricio F. de Oliveira , Pedro J. Tomaselli , José C. Nunez , Osvaldo J. M. do Nascimento , Amilton A. Barreira , Wilson Marques Jr Source Type: research

N ‐hexane exposure: a cause of small fiber neuropathy
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 26, 2018 Category: Neurology Source Type: research

Severe cognitive impairment in a patient with CMT2A
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 26, 2018 Category: Neurology Source Type: research

Functional outcome measures for infantile Charcot ‐Marie‐Tooth disease: a systematic review
Journal of the Peripheral Nervous System, EarlyView. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 23, 2018 Category: Neurology Source Type: research

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Journal of the Peripheral Nervous System, Ahead of Print. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 23, 2018 Category: Neurology Source Type: research

Issue Information
Journal of the Peripheral Nervous System,Volume 23, Issue 1, Page 1-3, March 2018. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 14, 2018 Category: Neurology Source Type: research

2018 Peripheral Nerve Society Annual Meeting, July 22 –25, 2018
Journal of the Peripheral Nervous System,Volume 23, Issue 1, Page 4-4, March 2018. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 14, 2018 Category: Neurology Source Type: research

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Journal of the Peripheral Nervous System,Volume 23, Issue 1, Page 1-3, March 2018. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 14, 2018 Category: Neurology Source Type: research

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Journal of the Peripheral Nervous System,Volume 23, Issue 1, Page 4-4, March 2018. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 14, 2018 Category: Neurology Source Type: research

2018 Peripheral Nerve Society Annual Meeting, July 22 –25, 2018
(Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 14, 2018 Category: Neurology Tags: ANNOUNCEMENT Source Type: research

Issue Information
(Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 14, 2018 Category: Neurology Tags: ISSUE INFORMATION Source Type: research

Functional outcome measures for infantile Charcot ‐Marie‐Tooth disease: A systematic review
Abstract A functional outcome measure for infants (aged 0‐3 years) with Charcot‐Marie‐Tooth disease (CMT) is needed for upcoming disease‐modifying trials. A systematic review of outcome measures for infants with neuromuscular disorders was completed to determine if validated measures were available for the CMT infant population. We assessed 20,375 papers and identified seven functional outcome measures for infants with neuromuscular disorders. Six were developed and validated for Spinal Muscular Atrophy (SMA). There were no CMT‐specific outcome measures identified, however one (Motor Function Measure) assessed a ...
Source: Journal of the Peripheral Nervous System - March 9, 2018 Category: Neurology Authors: Melissa R. Mandarakas, Kristy J. Rose, Oranee Sanmaneechai, Manoj P. Menezes, Kathryn M. Refshauge, Joshua Burns Tags: RESEARCH REPORT Source Type: research

The genetic heterogeneity of hereditary transthyretin amyloidosis in a sample of the Brazilian population
ConclusionsOur study depicts a scenario of greater genetic heterogeneity among Brazilian hATTR patients with FAP. We expect that this number will grow fast over a short period of time, due to increasing availability of genetic tests, increasing knowledge of the disease and the multivariate origin of our population. (Source: Journal of the Peripheral Nervous System)
Source: Journal of the Peripheral Nervous System - March 9, 2018 Category: Neurology Authors: Carolina Lavigne ‐Moreira, Vanessa Daccach Marques, Marcus V Magno Gonçalves, Mauricio Fernandes de Oliveira, Pedro J Tomaselli, José Nunez, Osvaldo J Moreira do Nascimento, Amilton Antunes Barreira, Wilson Marques Tags: RESEARCH REPORT Source Type: research

N ‐hexane exposure: a cause of small fiber neuropathy
Abstract A 59‐year old woman presented with progressive paresthesias of all of her limbs for 4 years, associated with neuropathic pain, tingling in the tongue and allodynia, consistent with small‐fiber neuropathy (SFN). Several systemic symptoms and signs were found on clinical examination and laboratory work‐up. Neurological investigations including neurophysiologic test and skin biopsy supported the diagnosis of SFN. Chronic exposure to N‐hexane was then disclosed and suspected to be the cause of the disease. Following the discontinuation of chronic N‐hexane exposure, the patient had a progressive improvement o...
Source: Journal of the Peripheral Nervous System - March 1, 2018 Category: Neurology Authors: Raquel Guimar ães‐Costa, Yoland Schoindre, Arnaud Metlaine, Jean‐Pascal Lefaucheur, Jean‐Philippe Camdessanché, Thierry Maisonobe, Jean‐Marc Léger Tags: CASE REPORT Source Type: research