Incidental finding of cornea verticillata or lamellar inclusions in kidney biopsy: measurement of lyso-Gb3 in plasma defines between Fabry disease and drug-induced phospholipidosis
Publication date: Available online 3 October 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): J. Politei, J. Frabasil, C. Durand, S. Di Pietrantonio, A. Fernandez, V. Albertón, D. Velasques Rivas, R. Barriales-Villa, J. Larrañaga-Moreira, A.B. Schenone (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - October 5, 2020 Category: Molecular Biology Source Type: research

Cross-disease analysis of depression, ataxia and dystonia highlights a role for synaptic plasticity and the cerebellum in the pathophysiology of these comorbid diseases
Publication date: Available online 2 October 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Miaozhen Huang, Tom J. de Koning, Marina A.J. Tijssen, Dineke S. Verbeek (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - October 3, 2020 Category: Molecular Biology Source Type: research

Glutaredoxin-2 and Sirtuin-3 deficiencies impair cardiac mitochondrial energetics but their effects are not additive
Publication date: Available online 28 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Neoma T. Boardman, Baher Migally, Chantal Pileggi, Gaganvir S. Parmar, Jian Ying Xuan, Keir Menzies, Mary-Ellen Harper (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 29, 2020 Category: Molecular Biology Source Type: research

The secretome of senescent preadipocytes influences the phenotype and function of cells of the vascular wall
Publication date: Available online 28 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Mojtaba Parvizi, Zachary C. Ryan, Sanam Ebtehaj, Bonnie K. Arendt, Ian R. Lanza (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 29, 2020 Category: Molecular Biology Source Type: research

Mitochondrial Calcium Handling and Heart Disease in Diabetes Mellitus
Publication date: Available online 28 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Julieta Diaz-Juarez, Jorge A. Suarez, Wolfgang H. DIllmann, Jorge Suarez (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 29, 2020 Category: Molecular Biology Source Type: research

Effect of Alanine Supplementation on Oxalate Synthesis
Publication date: Available online 28 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Kyle D. Wood, Brian L. Freeman, Mary E. Killian, Win Shun Lai, Dean Assimos, John Knight, Sonia Fargue (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 29, 2020 Category: Molecular Biology Source Type: research

Donepezil provides neuroprotective effects against brain injury and Alzheimer's pathology under conditions of cardiac ischemia/reperfusion injury
Publication date: 1 January 2021Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, Volume 1867, Issue 1Author(s): Benjamin Ongnok, Thawatchai Khuanjing, Titikorn Chunchai, Sasiwan Kerdphoo, Thidarat Jaiwongkam, Nipon Chattipakorn, Siriporn C. Chattipakorn (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 29, 2020 Category: Molecular Biology Source Type: research

Age–related and atherosclerosis–related erythropathy in ApoE/LDLR−/− mice
Publication date: 1 December 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, Volume 1866, Issue 12Author(s): Jakub Dybas, Katarzyna Bulat, Aneta Blat, Tasnim Mohaissen, Aleksandra Wajda, Mateusz Mardyla, Magdalena Kaczmarska, Magdalena Franczyk-Zarow, Kamilla Malek, Stefan Chlopicki, Katarzyna M. Marzec (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 26, 2020 Category: Molecular Biology Source Type: research

Excessive ROS Production and Enhanced Autophagy Contribute to Myocardial Injury Induced by Branched-chain Amino Acids: Roles for the AMPK-ULK1 Signaling Pathway and α7nAChR
Publication date: Available online 24 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Yu-Jie Jiang, Si-Jia Sun, Wen-Xiang Cao, Xiu-Ting Lan, Min Ni, Hui Fu, Dong-Jie Li, Pei Wang, Fu-Ming Shen (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 25, 2020 Category: Molecular Biology Source Type: research

Evolutionary Artificial Intelligence Based Peptide Discoveries for Effective Covid-19 Therapeutics
Publication date: Available online 24 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Ritika Kabra, Shailza Singh (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 25, 2020 Category: Molecular Biology Source Type: research

Physical exercise and seizure activity
Publication date: Available online 24 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Ricardo Mario Arida (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 25, 2020 Category: Molecular Biology Source Type: research

Arsenic trioxide-increased MDCK cells proliferation requires activator protein 1-mediated increase of the sodium/proton exchanger 1 activity
Publication date: Available online 24 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Marcelo Cornejo, Daniel Mieres, Elías Blanco, Ana R. Beltrán, Jorge E. Araya, Gonzalo Fuentes, Manuel Figueroa, Cristian Labarca, Fernando Toledo, Marco A. Ramírez, Luis Sobrevia (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 25, 2020 Category: Molecular Biology Source Type: research

The anti-tumor agent, Dp44mT, promotes nuclear translocation of TFEB via inhibition of the AMPK-MTORC1 axis
Publication date: Available online 17 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): S. Krishan, S. Sahni, D.R. Richardson (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 18, 2020 Category: Molecular Biology Source Type: research

Activation of α7nACh receptor protects against acute pancreatitis through enhancing TFEB-regulated autophagy
Publication date: Available online 18 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Bin Li, Jianghong Wu, Jingpiao Bao, Xiao Han, Shuangjun Shen, Xin Ye, Juanjuan Dai, Zengkai Wu, Mengya Niu, Yan He, Jianbo Ni, Li Wen, Xingpeng Wang, Guoyong Hu (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 18, 2020 Category: Molecular Biology Source Type: research

Donepezil provides neuroprotective effects against brain injury and Alzheimer’s pathology under conditions of cardiac ischemia/reperfusion injury
Publication date: Available online 18 September 2020Source: Biochimica et Biophysica Acta (BBA) - Molecular Basis of DiseaseAuthor(s): Benjamin Ongnok, Thawatchai Khuanjing, Titikorn Chunchai, Sasiwan Kerdphoo, Thidarat Jaiwongkam, Nipon Chattipakorn, Siriporn C. Chattipakorn (Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease)
Source: Biochimica et Biophysica Acta (BBA) Molecular Basis of Disease - September 18, 2020 Category: Molecular Biology Source Type: research