Radiofrequency ablation for fascicular ventricular tachycardia causing tachycardiomyopathy and brief literature review
Sanjeev S Mukharjee, Soumya Kanti Mohapatra, Aritra Mukherji, Arnab De, Anil Kumar SinghiAnnals of Pediatric Cardiology 2021 14(1):99-104 A 10-years-old boy presented with a history of effort intolerance and palpitations for 4 months. His electrocardiogram showed wide complex tachycardia suggestive of fascicular ventricular tachycardia (VT). The echocardiogram showed moderate-to-severe left ventricular systolic dysfunction without any structural lesion. The tachycardia was unresponsive to adenosine and direct current cardioversion. It responded to oral verapamil. The electrophysiology study confirmed the tachycardia as le...
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Sanjeev S Mukharjee Soumya Kanti Mohapatra Aritra Mukherji Arnab De Anil Kumar Singhi Source Type: research

Staged interventional solution for a diagnostic dilemma caused by hypoplastic left ventricle with severe aortic arch hypoplasia
Santosh Wadile, Kothandam SivakumarAnnals of Pediatric Cardiology 2021 14(1):95-98 Duct dependent aortic arch obstruction with borderline left ventricular hypoplasia presents a diagnostic dilemma. If the left ventricle (LV) is adequate to sustain systemic cardiac output without a patent duct, arch obstruction is relieved surgically and duct is divided. Inadequate LVs do not tolerate duct division, and these patients need more complex Norwood type surgeries. However, catheter-based interventions for arch obstruction can retain ductal patency. The progressive changes in anatomy and physiology of a neonate who presented with...
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Santosh Wadile Kothandam Sivakumar Source Type: research

Transcatheter treatment of an unusual coronary arteriovenous malformation with a fistulous sac in the interventricular septum
We report a case of CAF with an unusually large fistulous sac within the interventricular septum. The fistula had connections with all the three major coronary arteries, namely, left anterior descending (LAD), left circumflex , and right coronary arteries but did not have any exit resulting in to and fro movement of blood within the sac and the feeding vessels. The patient was managed successfully by transcatheter coil embolization. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Anupama Nair Kshitij Sheth Rahul Sheth Bharat Dalvi Source Type: research

Overdrive suppression of postoperative sustained ventricular tachycardia by atrial pacing and its hemodynamic effect
We present a case of 1-year 5-month-old child who developed VT with low cardiac output syndrome with deranged hepatic function, who was managed efficiently using suppressive atrial pacing to ameliorate the effects of sustained VT. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Mohammed Sameer Sudip Dutta Baruah Sabarinath Menon Baiju Sasi Dharan Sowmya V Ramanan Javid S Raja Narayanan Namboodiri Source Type: research

Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario
We present a rare case of LQTS associated with patent ductus arteriosus in a child, and a unique approach was used in managing both conditions. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Javid Raja Sabarinath Menon Devarakonda Bhargava Venkata KP Unnikrishnan Narayanan Namboodiri Source Type: research

Catheter closure of a patent vertical vein after repair of an unusual total anomalous variant of pulmonary venous drainage
Paolo Ferrero, Isabelle Piazza, Nageswara Rao Koneti, Matteo CiuffredaAnnals of Pediatric Cardiology 2021 14(1):82-84 Total anomalous pulmonary venous drainage (TAPVD) encompasses a wide spectrum of anatomical variants. The infradiaphragmatic type is almost always obstructive owing to the interposition of intrahepatic resistances; since almost invariable, the vertical vein inserts on the portal venous system. On correction of this variant, the vertical vein might not be ligated to avoid postoperative pulmonary hypertension. We hereby describe an unusual case of infradiaphragmatic TAPVD, with a vertical vein connected to d...
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Paolo Ferrero Isabelle Piazza Nageswara Rao Koneti Matteo Ciuffreda Source Type: research

Persistent atypical atrial flutter after device closure of the atrial septal defect in a young man
We describe a case of persistent atypical atrial flutter following device closure of ASD in a young man and discuss the management strategy given the various underlying dilemmas. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Keerthika Ravella Shrikant Bhoskar Neeta Bachani Yash Lokhandwala Bharat Dalvi Source Type: research

Use of selexipag in a teenage patient with pulmonary arterial hypertension
We report the case of a teenage patient with idiopathic PAH who presented in World Health Organization functional Class IV and showed no clinical improvement with dual therapy. We added oral selexipag to the treatment regimen and observed substantial improvement in her quality of life at the short-time follow-up. Despite the lack of childhood data regarding the use of selexipag in pediatric patients with PAH, the use of this drug in the current teenage patient improved her quality of life and exercise capacity. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Nathalie Jeanne Magioli Bravo-Valenzuela Flavia Navarro Socrates Pereira Silva Source Type: research

Myocardial infarction due to thrombosis of native aorta late after Fontan procedure for hypoplastic left heart syndrome
We present three cases of NAR thrombus with embolization to the CA, resulting in myocardial infarction. Thromboembolic events are well-documented complications of Fontan physiology, and optimal prevention and treatment strategies are poorly defined. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Bhavi Patel Tacy Downing Lourdes Prieto Darline Santana-Acosta Source Type: research

Video-assisted thoracoscopic pacemaker lead placement in children with atrioventricular block
Conclusion: Thoracoscopic pacemaker lead placement may provide a potential alternative to the transthoracic approach of epicardial lead placement in children with AVB. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Sergey Termosesov Ekaterina Kulbachinskaya Ekaterina Polyakova Dmitriy Khaspekov Ivan Grishin Vera Bereznitskaya Maria Shkolnikova Source Type: research

Defining transposition: What have we learnt ?
We describe an unusual variant of transposition, in which despite the arterial roots being supported by morphologically inappropriate ventricles, the roots themselves were normally related, with the intrapericardial arterial trunks spiraling as they extended into the mediastinum. The specimen was identified following the re-categorization of our archive, and we subsequently conducted a detailed analysis of the underlying morphology. Using the principles of sequential segmental analysis, we compared the morphology with standard examples previously described. We show how it was the recognition of such hearts that promoted th...
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Max E Roderick Nikita Maria Adrian Crucean John Stickley David J Barron Robert H Anderson Source Type: research

Tetralogy of fallot with coronary crossing the right ventricular outflow tract: A tale of a bridge and the artery
Sachin Talwar, Sanjoy Sengupta, Supreet Marathe, Pradeep Vaideeswar, Balram Airan, Shiv Kumar ChoudharyAnnals of Pediatric Cardiology 2021 14(1):53-62 A coronary artery crossing the right ventricular outflow tract is a subset of a larger pathomorphological cohort known as an anomalous coronary artery (ACA) in the tetralogy of Fallot (TOF). The best possible outcome in a patient with TOF and ACA is decided by judicious selection of optimum preoperative investigative information, the timing of surgery, astute assessment of preoperative surgical findings, and appropriate surgical technique from a wide array of choices. In mo...
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Sachin Talwar Sanjoy Sengupta Supreet Marathe Pradeep Vaideeswar Balram Airan Shiv Kumar Choudhary Source Type: research

Clinical profiles and risk factors for early and medium-term mortality following heart transplantation in a pediatric population: A single-center experience
Conclusions: Excellent outcomes are possible after heart transplantation in a pediatric population even in a resource constrained environment of a developing economy. More efforts are needed to promote pediatric organ donation and patients need to be referred in better INTERMACS category for optimal outcomes. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Komarakshi R Balakrishnan Kemundel Genny Suresh Rao Ganapathy Krishnan Subramaniam Murali Krishna Tanguturu Ajay Arvind Veena Ramanan Jagdish Dhushyanthan K Ramasubramanian K Suresh Kumaran Gunalan Sellamuthu Mohan Rajam Senthil Mettur Pradeep Gnansekhara Source Type: research

Melody valve to replace the mitral valve in small children: Lessons learned
Conclusions: Mitral valve replacement with a Melody valve is feasible in infants, is reproducible, shows good immediate results, and offers the possibility of later dilatation. This technique offers a better solution compared to the existing alternatives for infants requiring a prosthetic mitral valve. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Vilius Dranseika Rene Pretre Oliver Kretschmar Hitendu Dave Source Type: research

Utility of late pulmonary artery banding in single-ventricle physiology: A mid-term follow-up
Conclusions: Late PA band in selected patients with SV physiology can have definite benefit in terms of correction of heart failure symptoms and subsequent conversion to BDG and can potentially change the natural history of disease both in terms of survival and quality of life. (Source: Annals of Pediatric Cardiology)
Source: Annals of Pediatric Cardiology - January 16, 2021 Category: Cardiology Authors: Aritra Mukherji Sanjiban Ghosh Nihar Pathak Jayita Nandi Das Nilanjan Dutta Debasis Das Amitabha Chattopadhyay Source Type: research