Granulomatosis with polyangiitis - the incomplete puzzle
Acta Reumatol Port. 2021 Oct-Dec;46(4):350-354.ABSTRACTGranulomatous with polyangiitis (GPA) is a necrotizing granulomatous vasculitis that mostly affects small-sized vessels. The disease can affect many organs, although renal and respiratory tract involvement are the most frequent and distinguishing features. Musculoskeletal manifestations have been reported in about 50% of patients and can occur as myalgia, oligoarthralgia/arthritis of large joints or polyarthralgia/arthritis of small joints. Infrequently musculoskeletal symptoms can be the first disease manifestation, and in this clinical scenario GPA diagnosis might be...
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Ana Catarina Duarte Ana Cordeiro Pedro Gon çalves Maria Jos é Santos Source Type: research
Large-vessel vasculitis induced by pegfilgrastim
We report a case of G-CSF associated LVV in a patient with breast cancer. While clear pathogenic mechanisms remain unknown, G-CSF may cause vasculitis due to inflammatory cytokines production. This adverse reaction should be recognized in patients with suggestive symptoms following the administration of pegfilgrastim. A 56-year-old woman with luminal B breast cancer who had undergone surgery and adjuvant chemotherapy, initially with paclitaxel, was started on a doxorubicin plus cyclophosphamide protocol, followed by supportive use of long-acting G-CSF pegfilgrastim. Following the administration of pegfilgrastim, the patien...
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Ryan Costa Silva Margarida Monteiro Ricardo Pereira Dias In ês Silva Joana Rodrigues Dos Santos T ânia Vassalo Joana Rosa Martins In ês Leite Catarina Abreu Joana Martins-Martinho Cristina Ponte Jos é Carlos Romeu L ígia Peixoto Source Type: research
How did we get here?
Acta Reumatol Port. 2021 Oct-Dec;46(4):295-296.NO ABSTRACTPMID:34962244 (Source: Acta Reumatologica Portuguesa)
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Jaime Cunha Branco Source Type: research
Do mobility exercises in different environments have different effects in ankylosing spondylitis?
CONCLUSIONS: Multidimensional functional mobility exercises performed either in water or on land are important in the management of pulmonary manifestations of AS.PMID:34962245 (Source: Acta Reumatologica Portuguesa)
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Baris Gurpinar Nursen Ilcin Sema Savci Nurullah Akkoc Source Type: research
Evolution of clinical, histological and serological features in a Primary Sj ὄgren´s Syndrome cohort and the limitations of the current classification criteria
CONCLUSION: The time of evolution of symptoms plays a fundamental role in the clinical, histological and serological profiles in PSS.PMID:34962246 (Source: Acta Reumatologica Portuguesa)
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Carmen Magdalena Gamboa-Alonso David Vega-Morales Janett Luzmila Riega-Torres Brenda Roxana V ázquez-Fuentes Luis Ángel Ceceñas-Falcón Gabriel Figueroa-Parra Jazzia Emily D íaz-Angulo Dionicio Ángel Galarza-Delgado Source Type: research
The aftermath of hip fragility fractures - are we missing out on osteoporosis treatment?"
CONCLUSION: We found a gap in osteoporosis treatment after a hip fragility fracture, similar to literature reports when no fracture liaison service is in place. We believe that the lack of such protocols, the low rate of "osteoporosis" or "fragility fracture" mentioning at hospital discharge, together with the under recognition at primary care level, contribute to this reality. The implementation of new measures is crucial to improve prevention and management of fragility fractures.PMID:34962247 (Source: Acta Reumatologica Portuguesa)
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Raquel Costa Joana Romano Andreia Moreira Duarte Dantas Pedro Ribeiro Mariana Agre Jo ão Correia Source Type: research
A multidisciplinary approach in psoriatic disease: the different models of dermatology-rheumatology collaborations in Portugal
This report aims to describe how these multidisciplinary clinics were developed, their characteristics, and the main obstacles to their implementation. Although the different hospitals adopted distinct functional models, a consensus respecting the minimal core set assessment for PsD in Multidisciplinary Dermatology/Rheumatology Clinics should comprise all disease manifestations and, if possible, quality of life. The main objective of these clinics is to achieve remission/minimal disease activity. Limitations to these multidisciplinary approaches are discussed, namely financial, time management, and human resources obstacle...
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Pedro Mendes-Bastos Patr ícia Nero Paulo Ferreira Alexandra Bernardo Anabela Barcelos Fernando M Pimentel Dos Santos Jo ão Sousa Maria Manuela Loureiro Sofia Magina Miguel Alpalh ão Joana Antunes Elsa Vieira-Sousa Source Type: research
The role of muscle in the susceptibility and progression of axial Spondyloarthritis: The MyoSpA Study Protocol
DISCUSSION: The innovative and multidisciplinary approaches of this project rely on the elucidation of myofascial physical properties in axSpA and also on the establishment of a biological signature that relates to specific muscle properties. This hitherto unstudied link between gene/protein signatures and muscle properties may enhance our understanding of axSpA physiopathology and reveal new and useful diagnostic and therapeutic targets.PMID:34962249 (Source: Acta Reumatologica Portuguesa)
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Atlas Mashayekhi Sardoo Agna Neto Rita Pinheiro Torres Santiago Rodrigues-Manica L úcia Domingues Carolina Lage Crespo Jo ão Lagoas-Gomes Vasco Mascarenhas C ésar S Mendes Antonio Galzerano S érgio Fernandes de Almeida Alexandre Sepriano Sofia Ramiro Source Type: research
Bone marrow edema syndrome: an unusual cause for spontaneous unrelentless bilateral knee pain
Acta Reumatol Port. 2021 Oct-Dec;46(4):360-362.ABSTRACTBone marrow edema syndrome is a rare disease with an unknown etiology, self-limited and usually associated with an indolent course, which can also generate severe pain with tremendous functional impairment. The authors present a case of a 19-year-old female patient with a progressive, non-traumatic and unrelentless pain involving both knees, requiring persistently walking aids and analgesic drugs. The imaging studies showed a bilateral distal femur and proximal tibia bone marrow edema in the magnetic resonance imaging. Finally, and after an extensive investigation with...
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Andr é Chambel Andr é Spranger Paulo Almeida Joaquim Soares do Brito Source Type: research
Clinical images of ENT involvement in ANCA associated Vasculitis
Acta Reumatol Port. 2021 Oct-Dec;46(4):363-364.NO ABSTRACTPMID:34962251 (Source: Acta Reumatologica Portuguesa)
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Raquel Freitas Henrique Teixeira Jorge Lopes Ricardo S ão Pedro Jorge Dentinho Pedro Gon çalves Ana Cordeiro Maria Jos é Santos Source Type: research
Abdominal pain in Systemic Lupus Erythematosus: About a rare cause
Acta Reumatol Port. 2021 Oct-Dec;46(4):365-367.ABSTRACTSystemic lupus erythematosus (SLE) is an autoimmune disease with potential multisystemic involvement. Mesenteric panniculitis (MP) has been described as a rare feature in patients with SLE. The authors present a case of a 26 years old patient with previous diagnosis of SLE presenting with abdominal pain and distension and a peri-umbilical mass. Imagological findings were compatible with MP and ganglion biopsy revealed inflammatory pattern. Corticosteroid therapy was initiated with a resolution of pain after 6 months of treatment, with image reevaluation showing improve...
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Mariana da Silva Leal Ana Carolina Pereira Renata Aguiar Anabela Barcelos Source Type: research
Urticariform reaction lupus-like induced by adalimumab: a rare adverse effect
Acta Reumatol Port. 2021 Oct-Dec;46(4):368-369.NO ABSTRACTPMID:34962253 (Source: Acta Reumatologica Portuguesa)
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Maria Helena Louren ço Ana Bento Silva In ês Silva Jaime C Branco Source Type: research
The Role of Medical Therapy in Refractory Pigmented Villonodular Synovitis
Acta Reumatol Port. 2021 Oct-Dec;46(4):370-371.NO ABSTRACTPMID:34962254 (Source: Acta Reumatologica Portuguesa)
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: In ês M Rodrigues Bruno Miguel Fernandes Mariana M Chaves Francisco Rego Costa L úcia Costa Miguel Bernardes Madalena Pimenta Source Type: research
The relevance of a multidisciplinary care in the management of patients with Osteogenesis Imperfecta
Acta Reumatol Port. 2021 Oct-Dec;46(4):372-373.NO ABSTRACTPMID:34962255 (Source: Acta Reumatologica Portuguesa)
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Raquel Freitas Sandra Sousa F átima Godinho Source Type: research
Granulomatosis with polyangiitis - the incomplete puzzle
Acta Reumatol Port. 2021 Oct-Dec;46(4):350-354.ABSTRACTGranulomatous with polyangiitis (GPA) is a necrotizing granulomatous vasculitis that mostly affects small-sized vessels. The disease can affect many organs, although renal and respiratory tract involvement are the most frequent and distinguishing features. Musculoskeletal manifestations have been reported in about 50% of patients and can occur as myalgia, oligoarthralgia/arthritis of large joints or polyarthralgia/arthritis of small joints. Infrequently musculoskeletal symptoms can be the first disease manifestation, and in this clinical scenario GPA diagnosis might be...
Source: Acta Reumatologica Portuguesa - December 28, 2021 Category: Rheumatology Authors: Ana Catarina Duarte Ana Cordeiro Pedro Gon çalves Maria Jos é Santos Source Type: research
