Langerhans cell histiocytosis in children with refractory diarrhoea and hypoalbuminaemia as the initial presentation: two case reports and a literature review
We describe the cases of two patients who initially presented with chronic... (Source: BMC Pediatrics)
Source: BMC Pediatrics - March 22, 2024 Category: Pediatrics Authors: Yi Cao, Qing-Qing Wu, Wei-Hui Yan, Li-Na Lu, Yi-Jing Tao, Hai-Xia Feng, Yi-Jing Chu, Wei Cai and Ying Wang Tags: Case Report Source Type: research
Cheerio Sign: Pulmonary Langerhans Cell Histiocytosis
Arch Bronconeumol. 2024 Mar 7:S0300-2896(24)00058-9. doi: 10.1016/j.arbres.2024.02.018. Online ahead of print.NO ABSTRACTPMID:38508925 | DOI:10.1016/j.arbres.2024.02.018 (Source: Archivos de Bronconeumologia)
Source: Archivos de Bronconeumologia - March 20, 2024 Category: Respiratory Medicine Authors: Alejandro Garc ía García Jorge Mora Pinilla Beatriz Raboso Moreno Mar ía Teresa Río Ramírez Araceli Abad Fern ández Source Type: research
Cheerio Sign: Pulmonary Langerhans Cell Histiocytosis
Arch Bronconeumol. 2024 Mar 7:S0300-2896(24)00058-9. doi: 10.1016/j.arbres.2024.02.018. Online ahead of print.NO ABSTRACTPMID:38508925 | DOI:10.1016/j.arbres.2024.02.018 (Source: Archivos de Bronconeumologia)
Source: Archivos de Bronconeumologia - March 20, 2024 Category: Respiratory Medicine Authors: Alejandro Garc ía García Jorge Mora Pinilla Beatriz Raboso Moreno Mar ía Teresa Río Ramírez Araceli Abad Fern ández Source Type: research
Infantile myofibromatosis in a 5-month-old boy
A 5-month-old boy presented with a solitary occipital growth. The lesion was of hard consistency, immobile, painless, measuring 2x3 cm with no relevant lymph node involvement. The overlying skin was intact. There was no relevant family history. Ultrasound scan revealed a bony lytic lesion. Initial CT and MRIs were suspicious of Langerhans cell histiocytosis. The lesion was indenting into cerebellar hemispheres, contacting but not indenting the venous sinuses (figure 1). No abnormal brain parenchymal signal was identified. Histopathology examination showed interlacing fascicles of spindle cells with myofibroblastic morpholo...
Source: Archives of Disease in Childhood - March 19, 2024 Category: Pediatrics Authors: Mohammad, O., Jacoby, J., Tighe, M. P. Tags: Miscellanea Source Type: research
Clinicopathological study of ophthalmic cutaneous and mucocutaneous non-langerhans cell histiocytic lesions
The “C group” of the histiocytic disorders is characterized by non-Langerhans-cell histiocytic lesions in the skin, mucosal surfaces, or both, out of which Juvenile xanthogranuloma (JXG) is the most common typ... (Source: BMC Ophthalmology)
Source: BMC Ophthalmology - March 19, 2024 Category: Opthalmology Authors: Hind Manaa Alkatan, Dalal R. Fatani, Azza M.Y. Maktabi and Tariq A. Alzahem Tags: Research Source Type: research
Diagnosis of cystic lung diseases: a position statement from the UK Cystic Lung Disease Rare Disease Collaborative Network
Conclusions
We suggest that this focused workup should be performed in all people with multiple lung cysts and would streamline referral pathways, help guide early treatment, management decisions, improve patient experience and reduce overall care costs. It could also potentially catalyse a national research database to describe these less well-understood and unidentified diseases, categorise disease phenotypes and outcomes, potentially leading to better prognostic data and generating a stronger platform to understand specific disease biology. (Source: Thorax)
Source: Thorax - March 15, 2024 Category: Respiratory Medicine Authors: Johnson, S. R., Shaw, D. E., Avoseh, M., Soomro, I., Pointon, K. S., Kokosi, M., Nicholson, A. G., Desai, S. R., George, P. M. Tags: Thorax State of the art review Source Type: research
Letterer-Siwe disease presenting with gastrointestinal and cutaneous manifestations
Dermatol Online J. 2023 Dec 15;29(6). doi: 10.5070/D329662996.ABSTRACTHistiocytosis is a set of distinct proliferative illnesses defined by the proliferation and infiltration of varied numbers of dendritic cells, macrophages, and monocytes in the afflicted tissues. The skin and other organs may be impacted by the inflammatory infiltration. It can occur at any age. The severity of the symptoms can range from mild to severe, depending on the degree and type of organ involvement. Although certain forms of histiocytosis can be fatal, others can be treated successfully without sequelae. Langerhans cell histiocytosis manifests i...
Source: Dermatol Online J - March 13, 2024 Category: Dermatology Authors: Antonina Sergeevna Stadnikova Walaa Fadhil Abbas Olga Borisovna Tamrazova Ekaterina Andreevna Pristanskova Irina Nikolaevna Zakharova Irina Vladimirovna Berezhnaya Dmitry Alexandrovich Skobeev Lyudmila Viktorovna Goncharova Source Type: research
Letterer-Siwe disease presenting with gastrointestinal and cutaneous manifestations
Dermatol Online J. 2023 Dec 15;29(6). doi: 10.5070/D329662996.ABSTRACTHistiocytosis is a set of distinct proliferative illnesses defined by the proliferation and infiltration of varied numbers of dendritic cells, macrophages, and monocytes in the afflicted tissues. The skin and other organs may be impacted by the inflammatory infiltration. It can occur at any age. The severity of the symptoms can range from mild to severe, depending on the degree and type of organ involvement. Although certain forms of histiocytosis can be fatal, others can be treated successfully without sequelae. Langerhans cell histiocytosis manifests i...
Source: Dermatol Online J - March 13, 2024 Category: Dermatology Authors: Antonina Sergeevna Stadnikova Walaa Fadhil Abbas Olga Borisovna Tamrazova Ekaterina Andreevna Pristanskova Irina Nikolaevna Zakharova Irina Vladimirovna Berezhnaya Dmitry Alexandrovich Skobeev Lyudmila Viktorovna Goncharova Source Type: research
Letterer-Siwe disease presenting with gastrointestinal and cutaneous manifestations
Dermatol Online J. 2023 Dec 15;29(6). doi: 10.5070/D329662996.ABSTRACTHistiocytosis is a set of distinct proliferative illnesses defined by the proliferation and infiltration of varied numbers of dendritic cells, macrophages, and monocytes in the afflicted tissues. The skin and other organs may be impacted by the inflammatory infiltration. It can occur at any age. The severity of the symptoms can range from mild to severe, depending on the degree and type of organ involvement. Although certain forms of histiocytosis can be fatal, others can be treated successfully without sequelae. Langerhans cell histiocytosis manifests i...
Source: Dermatol Online J - March 13, 2024 Category: Dermatology Authors: Antonina Sergeevna Stadnikova Walaa Fadhil Abbas Olga Borisovna Tamrazova Ekaterina Andreevna Pristanskova Irina Nikolaevna Zakharova Irina Vladimirovna Berezhnaya Dmitry Alexandrovich Skobeev Lyudmila Viktorovna Goncharova Source Type: research
Letterer-Siwe disease presenting with gastrointestinal and cutaneous manifestations
Dermatol Online J. 2023 Dec 15;29(6). doi: 10.5070/D329662996.ABSTRACTHistiocytosis is a set of distinct proliferative illnesses defined by the proliferation and infiltration of varied numbers of dendritic cells, macrophages, and monocytes in the afflicted tissues. The skin and other organs may be impacted by the inflammatory infiltration. It can occur at any age. The severity of the symptoms can range from mild to severe, depending on the degree and type of organ involvement. Although certain forms of histiocytosis can be fatal, others can be treated successfully without sequelae. Langerhans cell histiocytosis manifests i...
Source: Dermatol Online J - March 13, 2024 Category: Dermatology Authors: Antonina Sergeevna Stadnikova Walaa Fadhil Abbas Olga Borisovna Tamrazova Ekaterina Andreevna Pristanskova Irina Nikolaevna Zakharova Irina Vladimirovna Berezhnaya Dmitry Alexandrovich Skobeev Lyudmila Viktorovna Goncharova Source Type: research
Letterer-Siwe disease presenting with gastrointestinal and cutaneous manifestations
Dermatol Online J. 2023 Dec 15;29(6). doi: 10.5070/D329662996.ABSTRACTHistiocytosis is a set of distinct proliferative illnesses defined by the proliferation and infiltration of varied numbers of dendritic cells, macrophages, and monocytes in the afflicted tissues. The skin and other organs may be impacted by the inflammatory infiltration. It can occur at any age. The severity of the symptoms can range from mild to severe, depending on the degree and type of organ involvement. Although certain forms of histiocytosis can be fatal, others can be treated successfully without sequelae. Langerhans cell histiocytosis manifests i...
Source: Dermatol Online J - March 13, 2024 Category: Dermatology Authors: Antonina Sergeevna Stadnikova Walaa Fadhil Abbas Olga Borisovna Tamrazova Ekaterina Andreevna Pristanskova Irina Nikolaevna Zakharova Irina Vladimirovna Berezhnaya Dmitry Alexandrovich Skobeev Lyudmila Viktorovna Goncharova Source Type: research
Letterer-Siwe disease presenting with gastrointestinal and cutaneous manifestations
Dermatol Online J. 2023 Dec 15;29(6). doi: 10.5070/D329662996.ABSTRACTHistiocytosis is a set of distinct proliferative illnesses defined by the proliferation and infiltration of varied numbers of dendritic cells, macrophages, and monocytes in the afflicted tissues. The skin and other organs may be impacted by the inflammatory infiltration. It can occur at any age. The severity of the symptoms can range from mild to severe, depending on the degree and type of organ involvement. Although certain forms of histiocytosis can be fatal, others can be treated successfully without sequelae. Langerhans cell histiocytosis manifests i...
Source: Dermatol Online J - March 13, 2024 Category: Dermatology Authors: Antonina Sergeevna Stadnikova Walaa Fadhil Abbas Olga Borisovna Tamrazova Ekaterina Andreevna Pristanskova Irina Nikolaevna Zakharova Irina Vladimirovna Berezhnaya Dmitry Alexandrovich Skobeev Lyudmila Viktorovna Goncharova Source Type: research
Letterer-Siwe disease presenting with gastrointestinal and cutaneous manifestations
Dermatol Online J. 2023 Dec 15;29(6). doi: 10.5070/D329662996.ABSTRACTHistiocytosis is a set of distinct proliferative illnesses defined by the proliferation and infiltration of varied numbers of dendritic cells, macrophages, and monocytes in the afflicted tissues. The skin and other organs may be impacted by the inflammatory infiltration. It can occur at any age. The severity of the symptoms can range from mild to severe, depending on the degree and type of organ involvement. Although certain forms of histiocytosis can be fatal, others can be treated successfully without sequelae. Langerhans cell histiocytosis manifests i...
Source: Dermatol Online J - March 13, 2024 Category: Dermatology Authors: Antonina Sergeevna Stadnikova Walaa Fadhil Abbas Olga Borisovna Tamrazova Ekaterina Andreevna Pristanskova Irina Nikolaevna Zakharova Irina Vladimirovna Berezhnaya Dmitry Alexandrovich Skobeev Lyudmila Viktorovna Goncharova Source Type: research
Letterer-Siwe disease presenting with gastrointestinal and cutaneous manifestations
Dermatol Online J. 2023 Dec 15;29(6). doi: 10.5070/D329662996.ABSTRACTHistiocytosis is a set of distinct proliferative illnesses defined by the proliferation and infiltration of varied numbers of dendritic cells, macrophages, and monocytes in the afflicted tissues. The skin and other organs may be impacted by the inflammatory infiltration. It can occur at any age. The severity of the symptoms can range from mild to severe, depending on the degree and type of organ involvement. Although certain forms of histiocytosis can be fatal, others can be treated successfully without sequelae. Langerhans cell histiocytosis manifests i...
Source: Dermatol Online J - March 13, 2024 Category: Dermatology Authors: Antonina Sergeevna Stadnikova Walaa Fadhil Abbas Olga Borisovna Tamrazova Ekaterina Andreevna Pristanskova Irina Nikolaevna Zakharova Irina Vladimirovna Berezhnaya Dmitry Alexandrovich Skobeev Lyudmila Viktorovna Goncharova Source Type: research
Letterer-Siwe disease presenting with gastrointestinal and cutaneous manifestations
Dermatol Online J. 2023 Dec 15;29(6). doi: 10.5070/D329662996.ABSTRACTHistiocytosis is a set of distinct proliferative illnesses defined by the proliferation and infiltration of varied numbers of dendritic cells, macrophages, and monocytes in the afflicted tissues. The skin and other organs may be impacted by the inflammatory infiltration. It can occur at any age. The severity of the symptoms can range from mild to severe, depending on the degree and type of organ involvement. Although certain forms of histiocytosis can be fatal, others can be treated successfully without sequelae. Langerhans cell histiocytosis manifests i...
Source: Dermatol Online J - March 13, 2024 Category: Dermatology Authors: Antonina Sergeevna Stadnikova Walaa Fadhil Abbas Olga Borisovna Tamrazova Ekaterina Andreevna Pristanskova Irina Nikolaevna Zakharova Irina Vladimirovna Berezhnaya Dmitry Alexandrovich Skobeev Lyudmila Viktorovna Goncharova Source Type: research
