Muscle Function and Physical Activity in the Modern Era of Cystic Fibrosis
Conditions: Cystic Fibrosis Interventions: Other: Volumetric ultrasound of the quadriceps and fitting of an accelerometer Sponsors: Hospices Civils de Lyon Not yet recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - February 9, 2024 Category: Research Source Type: clinical trials

Cardiopulmonary Fitness in Children With Cystic Fibrosis Compared to Healthy Children
Conditions: Cystic Fibrosis in Children Interventions: Diagnostic Test: VO2 max assessment Sponsors: University Hospital, Montpellier Completed (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - February 5, 2024 Category: Research Source Type: clinical trials

Hypertonic Saline in NCFB
Conditions: Bronchiectasis; Non-cystic Fibrosis Bronchiectasis Interventions: Drug: 7% Hypertonic Saline via nebulization Sponsors: University of North Carolina, Chapel Hill; Cystic Fibrosis Foundation Not yet recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - February 5, 2024 Category: Research Source Type: clinical trials

Single Dose Escalation Study of TR02 (Sustained Lipid Inhalation Technology [SLIT ™] Amikacin) in Participants With Cystic Fibrosis (CF) Having Chronic Infections of Pseudomonas Aeruginosa
Conditions: Cystic Fibrosis Interventions: Drug: SLIT ™ Amikacin; Drug: Placebo Sponsors: Insmed Incorporated Completed (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - February 2, 2024 Category: Research Source Type: clinical trials

Simeox Therapy at Home Versus Standard of Care in NCFB Patients With CMH
Conditions: Non-cystic Fibrosis Bronchiectasis; Chronic Mucus Hypersecretion Interventions: Device: Simeox; Combination Product: Control Sponsors: Physio-Assist; Medical University of Lodz; University Hospital in Krakow Recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - February 1, 2024 Category: Research Source Type: clinical trials

Analysis of Remote Monitoring/Virtual Clinic Data in Adult Patients With Cystic Fibrosis (Project Breathe)
Conditions: Cystic Fibrosis Interventions: Other: non interventional Sponsors: Papworth Hospital NHS Foundation Trust; Innovate UK; Cystic Fibrosis Trust; US Cystic Fibrosis Foundation Recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - January 25, 2024 Category: Research Source Type: clinical trials

A Phase 1, Single-Center Study Evaluating the Safety and Tolerability of RCT2100 in Healthy Participants
Conditions: Cystic Fibrosis Interventions: Drug: RCT2100; Other: Placebo Sponsors: ReCode Therapeutics Not yet recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - January 25, 2024 Category: Research Source Type: clinical trials

Safety, Tolerability, and Pharmacokinetics of SPL84 in Healthy Volunteers
Conditions: Cystic Fibrosis Interventions: Drug: SPL84; Other: Placebo Sponsors: SpliSense Ltd. Completed (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - January 23, 2024 Category: Research Source Type: clinical trials

Skeletal Health and Bone Marrow Composition in Adolescents With Cystic Fibrosis
Conditions: Cystic Fibrosis Interventions: Diagnostic Test: Magnetic resonance relaxometry; Diagnostic Test: Magnetic resonance spectroscopy; Diagnostic Test: Blood Draw; Diagnostic Test: DXA; Diagnostic Test: pQCT Sponsors: Boston Children ' s Hospital; Cystic Fibrosis Foundation Not yet recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - January 22, 2024 Category: Research Source Type: clinical trials

Evaluation of the efficiency of nanomicellar formulation of fat-soluble vitamins in patients with cystic fibrosis: the study protocol for a randomized controlled trial
DiscussionDue to persistent fat-soluble vitamin deficiency in CF disease, the nanomicelle formulation could be proposed as a new delivery method of fat-soluble vitamins in the treatment of cystic fibrosis.Trial registrationIranian Registry of Clinical Trials IRCT20220415054541N1. Registered on July 23, 2022. (Source: Trials)
Source: Trials - January 16, 2024 Category: Research Source Type: clinical trials

Renal Impact of KAFTRIO in Mucoviscidose Population
Conditions: Cystic Fibrosis Interventions: Biological: Evaluation of the parameters of the lithiasis assessment before and after KAFTRIO initiation; Drug: Collection of Arterial pressure, metabolic data, kidney function, proteinuria and hematuria before and after KATRIO initiation Sponsors: Hospices Civils de Lyon Recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - January 9, 2024 Category: Research Source Type: clinical trials

Sinus Disease in Young Children With Cystic Fibrosis
Conditions: Cystic Fibrosis in Children; Cystic Fibrosis; Chronic Rhinosinusitis (Diagnosis); Olfactory Disorder; Olfactory Impairment Interventions: Drug: Ivacaftor or elexacaftor/tezacaftor/ivacaftor Sponsors: University of California, Los Angeles; University of Kansas Medical Center; Children ' s Hospital Medical Center, Cincinnati; University of Iowa; University of Virginia; Children ' s Hospital Colorado; University of Vermont Recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - January 4, 2024 Category: Research Source Type: clinical trials

Viral Infections and Airway Microbiome in Young Children With Cystic Fibrosis
Conditions: Cystic Fibrosis in Children; Respiratory Bacterial Infection; Respiratory Viral Infection; Inflammation Lungs; Respiratory Morbidity Sponsors: University Hospital, Antwerp Enrolling by invitation (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - January 3, 2024 Category: Research Source Type: clinical trials

Evolution of the 6-minute Walk Test in Patients Treated With ELEXACAFTOR / TEZACAFTOR / IVACAFTOR
Conditions: Cystic Fibrosis Interventions: Other: 6-minute walk test Sponsors: Hospices Civils de Lyon Active, not recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - December 28, 2023 Category: Research Source Type: clinical trials

Assessment of Cognitive Function and Exercise Capacity in Cystic Fibrosis
Conditions: Cystic Fibrosis Sponsors: Hacettepe University Recruiting (Source: ClinicalTrials.gov)
Source: ClinicalTrials.gov - December 18, 2023 Category: Research Source Type: clinical trials