Temporal trends in healthcare resource use and associated costs of patients with cystic fibrosis
Cystic fibrosis (CF) is an autosomal recessive genetic disease caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene [1]. CFTR protein dysfunction induces a multisystem disease including respiratory manifestations and pancreatic, liver and gastrointestinal diseases. The prognosis remains dominated by the pulmonary manifestations leading to respiratory exacerbations and lung function decline [1].
Source: Journal of Cystic Fibrosis - Category: Respiratory Medicine Authors: Isabelle Durieu, Faustine Dalon, Quitterie Reynaud, Lydie Lemonnier, Cl émence Dehillotte, Marjorie Bérard, Déborah Walther, Marie Viprey, Eric Van Ganse, Manon Belhassen Tags: Original Article Source Type: research
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