Subclavian artery aneurysmal rupture and left internal mammary artery extravasation secondary to advanced Marfan syndrome

This case highlights the unusual life-threatening findings found in a patient with Marfan syndrome (MFS) in the emergency department setting. MFS is a rare autosomal dominant disease that affects 1 in 3000 –5000 individuals and has a highly variable range of clinical severity.This case is a 63-year-old male with COPD, scoliosis, aortic and mitral valve replacements on warfarin, and MFS who presented with acute onset hemoptysis, tachypnea, and oxygen saturation of 77% on 4 l nasal cannula. Emergent chest computed tomography angiography (CTA) revealed both a contained rupture of a left subclavian artery aneurysm and active extravasation from his left internal mammary artery (LIMA) into his left chest.
Source: The American Journal of Emergency Medicine - Category: Emergency Medicine Authors: Source Type: research