Lessons learned from surgical management of craniovertebral instability in Morquio syndrome: A series of four unusual cases

We present a series of four cases (mean age 4.3 ± 0.4 years) operated through posterior-only approach (n = 2, C1-lateral mass to C2 pars-interarticularis [Goel's technique]; n = 1 sublaminar wiring followed by C1-lateral mass to C2 pars-interarticularis; and n = 1 suboccipital plate with pars-interarticularis of C2 screw and pedicle of C3 and rod fixation). All patients had acceptable outcome and doing well at the last follow-up (12–96-follow-up). None of our patient needed transoral decompression. Patients with MS frequently manifest with spastic quadriparesis at an early age due to reducible AAD. Early surgical fixation with posterior C1–C2 screw and rod technique is recommended for the favorable surgical outcome and long-term stability of the cervical spine.

Source: Journal of Craniovertebral Junction and Spine - August 13, 2020 Category: Orthopaedics Authors: Suyash Singh Jayesh Sardhara Vandan Raiyani Arun Kumar Srivastava Sanjay Behari Source Type: research