Malformations Associated With Pediatric Congenital Cholesteatomas

Objective: To describe malformations associated with pediatric congenital cholesteatomas of the middle ear. Study Design: Retrospective study. Setting: Tertiary referral center. Patients: One hundred and seventy-three cases of middle ear congenital cholesteatoma (CC) in 171 children operated between 2007 and 2017. Interventions: Demographic, clinical, and surgical data were collected from operative reports. Main Outcome Measures: We first described the type and rate of malformations associated with CC. Secondly, we compared cholesteatoma features in two subgroups: anterior superior (AS) versus posterior superior (PS) starting point. Third, we compared demographic, clinical, and surgical data between patients with and without malformation. Results: CC was associated with malformations in 17 cases (17/173; 9.8%). The main malformation was preauricular fistula (8/173; 4.6%). Other malformations were: one first branchial cleft, two labio palatine cleft, one nasal cyst, two preauricular fibrochondroma, and five other malformations. PS congenital cholesteatomas were diagnosed in older children (4.6 versus 8.6 years, p 
Source: Otology and Neurotology - Category: ENT & OMF Tags: PEDIATRIC OTOLOGY Source Type: research