A Rare Case of Vena Cava Tumor Thrombus Associated with Epithelioid Angiomyolipoma

Renal angiomyolipoma (AML) is a benign, mesenchymal tumor consisting of mature adipose tissue, thick-walled blood vessels, and spindle smooth muscle-like cells. Although the majority of AMLs arise sporadically, they are seen in 50-90% of patients with Tuberous Sclerosis Complex (TSC). In the absence of symptoms or concern for malignancy, AML is managed conservatively with the priority of maintaining kidney function. Tumors ≤4 cm typically undergo observation with annual imaging. Selective renal arterial embolization or partial nephrectomies are performed for indications such as hemorrhage, bleeding, and/or suspicion of malignancy.
Source: Urology - Category: Urology & Nephrology Authors: Tags: Grand Rounds Source Type: research