Anesthetic Management of Pediatric Patients with Niemann-Pick Disease Type C for Intrathecal 2-hydroxypropyl- β-cyclodextrin Injection.

CONCLUSIONS: Our findings suggest that general anesthesia induced via inhalation induction and maintained with volatile anesthetic via mask or supraglottic airway is a safe andeffective option for pediatric patients with Niemann-Pick disease type C undergoing serial intrathecal injections of 2-hydroxypropyl-beta-cyclodextrin, supporting thistechnique as a viable option for anesthetic care in these patients. PMID: 32349180 [PubMed - as supplied by publisher]

https://www.ncbi.nlm.nih.gov/pubmed/32349180?dopt=Abstract

Source: Paediatric Anaesthesia - April 28, 2020 Category: Anesthesiology Authors: Ulloa ML, Froyshteter AB, Kret LN, Chang DP, Sarah GE, McCarthy RJ, Barnes SD, Berry-Kravis EM Tags: Paediatr Anaesth Source Type: research