Anesthetic Management of a Pediatric Patient With Cardiofaciocutaneous Syndrome.

Anesthetic Management of a Pediatric Patient With Cardiofaciocutaneous Syndrome. Anesth Prog. 2020;67(1):45-47 Authors: Shionoya Y, Yamamoto M, Sunada K, Nakamura K Abstract Cardiofaciocutaneous (CFC) syndrome is a rare condition characterized by congenital heart disease, craniofacial dysmorphology, and dermatological abnormalities. CFC syndrome is one of the RASopathies, a family of syndromes that also includes Noonan and Costello syndromes, all with underlying gene mutations involving the Ras/mitogen-activated protein kinase pathways. Important considerations for anesthesiologists caring for these patients include the need to evaluate for possible cardiac defects, anticipating and planning for potentially difficult airway management, and the consideration of potential weakness of the respiratory muscles. Musculoskeletal abnormalities, such as muscle weakness and decreased muscle mass, are observed in all RASopathies, but are particularly prominent in CFC syndrome. In patients with CFC syndrome who experience respiratory muscle weakness, the use of desflurane and remifentanil may aid in a faster recovery and effectively help reduce the risk of respiratory complications, such as respiratory depression, following general anesthesia because of their rapid metabolism or elimination. PMID: 32191511 [PubMed - in process]
Source: Anesthesia Progress - Category: Anesthesiology Tags: Anesth Prog Source Type: research

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Hi! There really isn't much information out there regarding dental anesthesiology, so I figured I'd start the thread this year to hopefully connect with other applicants. Feel free to share any info or post any questions Good luck everybody! Previous threads: **Official 2020 Dental Anesthesiology PASS/Interviews/Match**... **Official 2021 Dental Anesthesiology PASS/Interviews/Match**
Source: Student Doctor Network - Category: Universities & Medical Training Authors: Tags: Dental Residents and Practicing Dentists Source Type: forums
CONCLUSION: Platelet count and serotonin concentration did not prove to be of diagnostic value in differentiating patients and healthy individuals. However, illness duration in patients with schizophrenia may be associated with reduced concentrations of platelet serotonin. PMID: 32492767 [PubMed - as supplied by publisher]
Source: Psychiatry Investigation - Category: Psychiatry Tags: Psychiatry Investig Source Type: research
CONCLUSIONS: Acute normovolemic hemodilution, in scoliosis correction surgeries reduces blood transfusion rates, meeting patient needs without increasing adverse events or infection rates. PMID: 32493689 [PubMed - as supplied by publisher]
Source: Revista Brasileira de Anestesiologia - Category: Anesthesiology Tags: Rev Bras Anestesiol Source Type: research
Authors: Allary C, Caruselli M, Fabre A, Audic F, Michel F Abstract Crisponi syndrome is a rare and severe heritable disorder characterised by muscle contractions, trismus, apnea, feeding troubles, and unexplained high fever spikes with multiple organ failure. Here we report perioperative care for endoscopic gastrostomy of a 17 month-old female child with Crisponi syndrome. Temperature in the surgery room was strictly monitored and maintained at 19°C. The patient was exposed to both inhaled and intravenous anesthetic agents. Surgical and perioperative periods were uneventful. Episodes of fever in...
Source: Revista Brasileira de Anestesiologia - Category: Anesthesiology Tags: Rev Bras Anestesiol Source Type: research
Authors: Saito I PMID: 32493882 [PubMed - as supplied by publisher]
Source: Journal of Atherosclerosis and Thrombosis - Category: Cardiology Tags: J Atheroscler Thromb Source Type: research
What is the expected intubation skill level for an incoming EM intern? Pre-COVID I had the chance to do an M4 anesthesia rotation for a couple of weeks before COVID fully hit and rotations got cancelled for the rest of the year. I'd say my proficiency rate was about 50% and even then most of the ones I managed to get weren't first pass, and these were on relatively normal/healthy patients that the CRNAs let me attempt.
Source: Student Doctor Network - Category: Universities & Medical Training Authors: Tags: Emergency Medicine Source Type: forums
CONCLUSIONS In this Caribbean population, uncontrolled asthma was independently associated with obesity, late-onset disease, and comorbidities of sleep apnea and depression. Poor asthma-related quality of life was independently associated with Indo-Caribbean ethnicity. PMID: 32493146 [PubMed - as supplied by publisher]
Source: Journal of Asthma - Category: Respiratory Medicine Tags: J Asthma Source Type: research
Conclusion: Observations here demonstrate a potentially useful technical strategy toward clearance of proximal shunt obstructions, in situ. PMID: 32494391 [PubMed]
Source: Surgical Neurology International - Category: Neurosurgery Tags: Surg Neurol Int Source Type: research
Publication date: Available online 4 June 2020Source: Annals of Emergency MedicineAuthor(s): Michael Gottlieb, Shayna Adams, Richard R. Treviño
Source: Annals of Emergency Medicine - Category: Emergency Medicine Source Type: research
CONCLUSION: Smoking and symptoms of adjustment disorder, specifically preoccupations, are associated with functional outcome 1 year post-operation in patients recovering from ankle or lower leg fractures. The results support the notion that differences in functional recovery are attributable to psychological and behavioural factors rather than to fracture type. Psychological, fracture-specific, symptoms play a role in functional recovery rather than general affective symptoms. PMID: 32495846 [PubMed - as supplied by publisher]
Source: Journal of Rehabilitation Medicine - Category: Rehabilitation Tags: J Rehabil Med Source Type: research
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