Hidradenitis suppurativa in a female adolescent with Rett syndrome: a fortuitous association?
Hidradenitis suppurativa in a female adolescent with Rett syndrome: a fortuitous association? G Ital Dermatol Venereol. 2020 Mar 10;: Authors: Provvidenziale L, Cinotti E, Campoli M, Russo F, Rubegni P PMID: 32163043 [PubMed - as supplied by publisher]
ConclusionsHS patients show a broad spectrum of inflammatory and metabolic syndrome-related comorbidities, with an increased risk by concurrent PsO. Important for clinical practice, the elevated cardiovascular risk of HS patients can be largely attributed to smoking.
The article by Hou et al.  evaluated item and score distributions and test-retest reliability for the Rett Syndrome Behaviour Questionnaire (RSBQ)  in 149 patients with Rett syndrome (RTT). The authors report that total, but not domain scores were normally distributed and Cronbach alpha values indicated good internal consistency. However, the scale had poor test-retest reliability and approximately half of the items exhibited floor or ceiling effects.
The 4th Annual Symposium on Hidradenitis Suppurativa (SHSA) took place on 1-3 November 2019 at the Westin Book Cadillac Hotel in Detroit, Michigan, U.S.A. This symposium was a joint meeting of the United States Hidradenitis Suppurativa Foundation (HSF) and the Canadian Hidradenitis Suppurativa Foundation (CHSF). This cross- disciplinary meeting with experts from around the world was an opportunity to discuss the most recent advances in the study of hidradenitis suppurativa (HS) pathogenesis, clinical trials, classification, scoring systems, complementary/ alternative medical treatments (CAM), diet, pain management, surgica...
What Is the Life Expectancy of a Person with Rett Syndrome?
PMID: 32476130 [PubMed - as supplied by publisher]
Abstract Hidradenitis suppurativa (HS), also known as acne inversa, is a chronic inflammatory disorder of the pilosebaceous units. To date, studies on the risk of keratinocyte carcinoma (KC), defined as basal cell carcinoma (BCC) and squamous cell carcinoma (SCC), among HS patients have been limited. We performed a case-control study comparing the incidence of BCC and SCC in HS patients (cases) to that in acne vulgaris patients (controls), which is also an inflammatory disorder of the pilosebaceous unit. PMID: 32473027 [PubMed - as supplied by publisher]
In their recent publication Assan et al1 have shown that both IgG and IgA anti–Saccharomyces cerevisiae antibodies (ASCAs) are associated with hidradenitis suppurativa (HS).1 As the authors state, ASCA positivity has long been associated with Crohn disease and has recently been identified as a biomarker for spondyloarthritis (SpA). However, both Crohn disease and SpA comprise distinct phenotypes. The phenotype in Crohn disease can change from an inflammatory phenotype, to a fibrostenotic or penetrating phenotype with respectively severe stricturing or fistulation.
We read with interest the correspondence by van Straalen1 about our article reporting an association between anti –Saccharomyces cerevisiae antibodies (ASCAs) and hidradenitis suppurativa (HS), mainly in its severe and inflammatory forms, in comparison with healthy controls and severe psoriasis vulgaris.2
This population-based study examines the prevalence of cancer in patients with hidradenitis suppurativa.