Cystic Fibrosis Foundation consensus guidelines for the care of individuals with advanced cystic fibrosis lung disease

While the quality of life and survival of individuals with cystic fibrosis (CF) are improving, advanced CF lung disease (ACFLD) remains common and the most frequent cause of death. CF Foundation Patient Registry data show that the forced expiratory volume in one second (FEV1) is less than 40 percent predicted in 18% of patients who are age 30 years, and nearly 25% of those age 45 years. ACFLD is associated with reduced quality of life, worsening clinical symptoms, increased exacerbations, and increased healthcare utilization [1,2].

Source: Journal of Cystic Fibrosis - February 26, 2020 Category: Respiratory Medicine Authors: Siddhartha G. Kapnadak, Emily Dimango, Denis Hadjiliadis, Sarah E. Hempstead, Erin Tallarico, Joseph M. Pilewski, Albert Faro, James Albright, Christian Benden, Shaina Blair, Elisabeth P. Dellon, Daniel Gochenour, Peter Michelson, Baharak Moshiree, Isabel Source Type: research