Oral Manifestations and Challenges in Dental Treatment of Epidermolysis Bullosa Dystrophica

Source: Journal of Dentistry for Children - Category: Dentistry Authors: Tags: Case Reports Source Type: research

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We present three patients with EB who were prescribed pharmaceutical‐grade sublingually administered CBMs comprising tetrahydrocannabinol and cannabidiol. All three patients reported improved pain scores, reduced pruritus and reduction in overall analgesic drug int ake.
Source: British Journal of Dermatology - Category: Dermatology Authors: Tags: Case Report: Therapy Source Type: research
PMID: 30413238 [PubMed - in process]
Source: Skinmed - Category: Dermatology Authors: Tags: Skinmed Source Type: research
This retrospective study looks at bone mineral density of people with recessive dystrophic epidermolysis bullosa as assessed by dual ‐energy x‐ray absorptiometry. Data were collected in 34 patients aged 16‐35 years. Statistical analysis showed immobility, low body mass index, and pubertal delay was associated with osteoporosis. Key Clinical MessageThis retrospective study looks at bone mineral density of people with recessive dystrophic epidermolysis bullosa as assessed by dual ‐energy x‐ray absorptiometry. Data were collected in 34 patients aged 16‐35 years. Statistical analysis showed immobility, lo...
Source: Clinical Case Reports - Category: General Medicine Authors: Tags: CASE REPORT Source Type: research
Rare diseases affect approximately 30 million people in the European Union and present a major health issue. Over 1000 rare skin diseases are known, many of which are of genetic origin and manifest in childhoo...
Source: Orphanet Journal of Rare Diseases - Category: Internal Medicine Authors: Tags: Research Source Type: research
Journal of Wound Care,Volume 27, Issue 11, Page 768-771, November 2018.
Source: Journal of Wound Care - Category: Nursing Authors: Source Type: research
Condition:   Epidermolysis Bullosa Interventions:   Drug: Ropivacaine;   Biological: Blood test Sponsor:   Assistance Publique - Hôpitaux de Paris Not yet recruiting
Source: ClinicalTrials.gov - Category: Research Source Type: clinical trials
Generalized severe epidermolysis bullosa simplex (EBS-gen sev) is caused by mutations within either the KRT5 or KRT14 gene, phenotypically resulting in blistering and wounding of the skin and mucous membranes aft...
Source: Orphanet Journal of Rare Diseases - Category: Internal Medicine Authors: Tags: Letter to the Editor Source Type: research
The heritable forms of epidermolysis bullosa (EB), a phenotypically heterogeneous group of skin fragility disorders, is currently associated with mutations in as many as 21 distinct genes. EB is primarily a disorder affecting the epithelial layers of skin and mucous membranes, without extracutaneous manifestations, and thus being non-syndromic. However, recent demonstrations of skin blistering in the spectrum of EB in multisystem disorders with single gene defects highlight the concept of syndromic EB.
Source: Journal of Investigative Dermatology - Category: Dermatology Authors: Tags: Perspective Source Type: research
Journal of the European Academy of Dermatology and Venereology,Volume 0, Issue ja, -Not available-.
Source: Journal of the European Academy of Dermatology and Venereology - Category: Dermatology Authors: Source Type: research
Journal of the European Academy of Dermatology and Venereology,Volume 0, Issue ja, -Not available-.
Source: Journal of the European Academy of Dermatology and Venereology - Category: Dermatology Authors: Source Type: research
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