P.05Feasibility and validation of modified oculobulbar facial respiratory score (mOBFRS) in sporadic inclusion body myositis

Sporadic inclusion body myositis (sIBM) is a neurodegenerative disorder that results in progressive limb muscle weakness with bulbar and respiratory involvement. The leading cause of morbidity and mortality are secondary to bulbar dysfunction. The IBMFRS is a reliable patient reported outcome measure used in sIBM, however, we lack objective scales that can quantitate deterioration in bulbar function in a clinic setting. We are conducting a prospective study to test the feasibility of using,and validate the use of the modified oculobulbar facial respiratory score (mOBFRS) in sIBM.
Source: Neuromuscular Disorders - Category: Neurology Authors: Source Type: research