An unusual association of sinus of Valsalva aneurysm with pulmonary atresia and intact ventricular septum

A 17-year-old female, having previously undergone bidirectional Glenn shunt surgery 10 years back, presented with complaints of gradually progressive dyspnea on exertion for the past 3 months with episodes of bilateral pedal swelling. Sheunderwent a cardiac computed tomography angiography which demonstrated tricuspid atresia with hypoplastic and hypertrophied right ventricle (RV) and atrial septal defect (Supplementary video files 1 –2). There was associated membranous pulmonary atresia (PA, dotted circle) (Fig.
Source: Journal of Cardiovascular Computed Tomography - Category: Radiology Authors: Tags: Case report Source Type: research