Persistence of anti-envoplakin and anti-periplakin antibodies in a case of Paraneoplastic Pemphigus 20 years after remission.

Persistence of anti-envoplakin and anti-periplakin antibodies in a case of Paraneoplastic Pemphigus 20 years after remission. Br J Dermatol. 2019 Sep 16;: Authors: Riera-Monroig J, Iranzo P, Ishii N, Hashimoto T, Mascaró JM Abstract Paraneoplastic pemphigus (PNP), also known as Paraneoplastic Autoimmune Multiorgan Syndrome (PAMS) is an autoimmune blistering disease associated with neoplasms, especially lymphoproliferative disorders. Early case reports and series described a poor prognosis. In a recent review of all reported patients until 2016, first year survival rate was 62.4%.1 Here, we describe the long survival of a previously reported case,2 to whom serologic studies were performed during follow-up. PMID: 31529517 [PubMed - as supplied by publisher]
Source: The British Journal of Dermatology - Category: Dermatology Authors: Tags: Br J Dermatol Source Type: research