A rare form of Mayer-Rokitansky-Küster-Hauser syndrome: Case report and review of literature

ConclusionMRKH syndrome with bilateral rudimentary uterine horns and normal-length vagina is an unusual form of Müllerian agenesis.
Source: Case Reports in Womens Health - Category: OBGYN Source Type: research

Related Links:

Publication date: Available online 20 September 2019Source: Journal of Minimally Invasive GynecologyAuthor(s): Maria Tereza Pinto Medeiros Dias, Andreisa Paiva Monteiro Bilhar, Livia Cunha Rios, Bruno Almeida Costa, Edmar Maciel Lima Júnior, Ana Paula Negreiros Nunes Alves, Zenilda Vieira Bruno, Manoel Odorico de Moraes Filho, Leonardo Robson Pinheiro Sobreira BezerraABSTRACTMayer–Rokitansky–Kuster–Hauser syndrome is the second most common cause of primary amenorrhea, trailing only gonadal dysgenesis. In patients who failed dilation therapy, neovaginoplasty is an appropriate treatment option. Sever...
Source: Journal of Minimally Invasive Gynecology - Category: OBGYN Source Type: research
Mayer –Rokitansky–Kuster–Hauser syndrome is the second most common cause of primary amenorrhea, trailing only gonadal dysgenesis. In patients who failed dilation therapy, neovaginoplasty is an appropriate treatment option. Several biomaterials have been used in this procedure, including peritoneum, amnion, skin grafts and myocutaneous flaps. Nile Tilapia Fish Skin has non-infectious microbiota, morphological structure comparable to human skin, and high in vivo bioresorption. In addition, it showed good outcomes when used as a xenograft for burn treatment.
Source: The Journal of Minimally Invasive Gynecology - Category: OBGYN Authors: Tags: INSTRUMENTS AND TECHNIQUES Source Type: research
Mayer-Rokitansky-K üster-Hauser syndrome is the second most common cause of primary amenorrhea, trailing only to gonadal dysgenesis. Neovaginoplasty is an appropriate treatment option for patients who have failed dilation therapy. Several biomaterials have been used in this procedure, including peritoneum, amnion, sk in grafts, and myocutaneous flaps. Nile Tilapia Fish Skin has noninfectious microbiota, morphologic structure comparable to human skin, and high in vivo bioresorption. In addition, it showed good outcomes when used as a xenograft for burn treatment.
Source: The Journal of Minimally Invasive Gynecology - Category: OBGYN Authors: Tags: Instruments and Techniques Source Type: research
Conclusion: Quality of sexual life after the Vecchietti's operation in long-term follow-up does not differ from that of healthy women, but these patients suffer more frequent from urogynecological complaints. The trial is registered with NCT03809819. PMID: 30931323 [PubMed - in process]
Source: Biomed Res - Category: Research Authors: Tags: Biomed Res Int Source Type: research
CONCLUSION:: MRI is capable of providing key pre-operative anatomical information in MRKH syndrome non-invasively. There is good to excellent interobserver agreement for MRI features of most of the surgical relevant structures. ADVANCES IN KNOWLEDGE:: MRI features of salient preoperative anatomical structures are reproducible between observers. PMID: 30864823 [PubMed - as supplied by publisher]
Source: The British Journal of Radiology - Category: Radiology Authors: Tags: Br J Radiol Source Type: research
M üllerian aplasia or Mayer-Rokitansky-Küster-Hauser syndrome is described as congenital absence of the proximal vagina with or without absence of the cervix and uterus, most often recognized following the onset of primary amenorrhea.
Source: Journal of Pediatric and Adolescent Gynecology - Category: OBGYN Authors: Source Type: research
Conclusions The case presented is unique in that 2 rare pathologies, bilateral Sertoli cell tumors of the ovary and MRKH syndrome, developed concomitantly in the same patient.
Source: Journal of Pelvic Medicine and Surgery - Category: Surgery Tags: Case Reports Source Type: research
CONCLUSION(S)In the past, the uterus with a rudimentary cavity of the MRKH patients was always excised. And the patients lost the chance of menstrual onset and fertility. Combined laparoscopic and Wharton-Sheares-George cervicovaginal reconstruction using SIS graft provided a minimally invasive, safe, and effective surgical option for the young patient with MRKH syndrome with a rudimentary cavity. The technique is not complex and easy to learn and perform. And it provided a result with functional and anatomical satisfaction. No special surgical apparatus is needed.
Source: Journal of Minimally Invasive Gynecology - Category: OBGYN Source Type: research
CONCLUSION(S) In the past, the uterus with a rudimentary cavity of the MRKH patients was always excised. And the patients lost the chance of menstrual onset and fertility. Combined laparoscopic and Wharton-Sheares-George cervicovaginal reconstruction using SIS graft provided a minimally invasive, safe, and effective surgical option for the young patient with MRKH syndrome with a rudimentary cavity. The technique is not complex and easy to learn and perform. And it provided a result with functional and anatomical satisfaction. No special surgical apparatus is needed.
Source: Journal of Minimally Invasive Gynecology - Category: OBGYN Source Type: research
Authors: Kasap E, Gene M, Sahin N, Sivrikoz ON Abstract Milllerian agenesis and the absence of organs of Millerian canal origin are referred to as Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome. Invasive ductal carcinoma constitutes 47-75% of all breast carcinomas and is the most common type. The authors report the first case of invasive ductal carcinoma associated with MRKH syndrome in the literature to their knowledge. A 25-year-old woman with a palpable mass in her right breast for three months presented to the presented clinic. On physical examination a mobile, firm mass measuring 2x2 cm was detected in right b...
Source: European Journal of Gynaecological Oncology - Category: OBGYN Tags: Eur J Gynaecol Oncol Source Type: research
More News: Amenorrhea | Eyes | Hormones | Men | MRI Scan | MRKH Syndrome | OBGYN | Ovaries | Ultrasound | Women