Igg4-related ophthalmic disease presenting as choroidal and orbital lesions

Conclusion: IgG4-related disease is a systemic fibroinflammatory disease, which often presents in another location, as in our patient. In cases of uncertain choroidal and orbital lesions, a thorough workup for other etiologies is indicated, and lymphoma must be ruled out. Steroids are the mainstay of treatment for IgG4-ROD, however, small case series and our patient responded well to rituximab. To our knowledge, this is the first reported case of choroidal and orbital lesions secondary to IgG4-ROD.
Source: Retinal Cases and Brief Reports - Category: Opthalmology Tags: Case Report Source Type: research

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