Lymphangiomatosis of the ileum with perforation: A case report and review of the literature

Publication date: Available online 29 March 2019Source: Annals of Medicine and SurgeryAuthor(s): Antonio Giuliani, Lucia Romano, Gino Coletti, Mohammad Walid A Fatayer, Giuseppe Calvisi, Francesco Maffione, Chiara Muolo, Vincenzo Vicentini, Mario Schietroma, Francesco CarleiAbstractLymphangiomatosis is a benign proliferation of lymph vessels. Lymphatic diseases can vary from small lymphangioma to generalized lymphangiomatosis, which is a rare condition and can have several clinical manifestations. The gastrointestinal tract may be affected, but the incidence in the intestinal wall is very low. We propose in our study a case of ileal lymphangiomatosis presenting with perforation, in which the diagnosis was made after the pathological analysis of the resected intestinal tract. Although rare and not described in the literature, intestinal lymphangiomatosis could manifest itself with acute abdomen and could be a surgical urgency. This disease should be considered when intestinal perforation is observed.
Source: Annals of Medicine and Surgery - Category: General Medicine Source Type: research