Acid sphingomyelinase deficiency (Niemann-Pick disease type B) as an inflammatory disease

In this report, early graft dysfunction was diagnosed at day 3 and the patient was empirically treated with antibiotics and high dose corticosteroid therapy. Death occurred on the 29th post-operative day and an autopsy revealed abundance of foamy macrophages in lung tissue consistent with ASMD cells.

Source: The Journal of Heart and Lung Transplantation - February 16, 2019 Category: Transplant Surgery Authors: Olivier Lidove, Wladimir Mauhin, Jonathan London Tags: LETTER TO THE EDITOR Source Type: research