Cirrhosis associated with decreased survival and a 10-year lower median age at death of cystic fibrosis patients in the Netherlands

Up to 10% of patients with Cystic Fibrosis develop cirrhotic CF-related liver disease with portal hypertension: CF cirrhosis (CFC). In a nationwide study, we aimed to determine the role of CFC on survival in the Netherlands between 1 and 1-2009 and1-1-2015.

Source: Journal of Cystic Fibrosis - December 14, 2018 Category: Respiratory Medicine Authors: F.H. Pals, H.J. Verkade, V.A.M. Gulmans, B.A.E. De Koning, B.G.P. Koot, T.G.J. De Meij, D.M. Hendriks, N. Gierenz, A.C.E. Vreugdenhil, R.H.J. Houwen, F.A.J.A. Bodewes Source Type: research