Near-fatal presentation of bilateral pneumothorax in cutis laxa patient: Case report, and review of the literature

Waseem M Hajjar, Areej S Alrajeh, Lulwah S Alturki, Sami A Al-Nassar, Adnan W HajjarAnnals of Thoracic Medicine 2018 13(4):254-256Cutis laxa (CL) is a rare connective tissue disease characterized by a loose, wrinkled, and inelastic skin. Here, we report an unusual presentation in a 15-year-old male patient who is a known patient of CL who presented with bilateral pneumothorax. He was successfully managed initially by chest tube insertion and then he was treated surgically with bilateral staged thoracoscopy, apical bullectomy, and pleurodesis with full uneventful recovery.

Source: Annals of Thoracic Medicine - October 10, 2018 Category: Respiratory Medicine Authors: Waseem M Hajjar Areej S Alrajeh Lulwah S Alturki Sami A Al-Nassar Adnan W Hajjar Source Type: research