Harare children ’s hospital airway symposium and pentafrica conference 2018
The 2018 PENTAFRICA  conference began with a pre-congress airway workshop and symposium held at Harare Children's Hospital on May 21st and 22nd. The free workshop, sponsored by the Zimbabwe Society of Otolaryngology, started with a day of airway surgeries, including cases of laryngeal atresia, laryngeal cleft, vocal cord paralysis, laryngomalacia, RRP, attended by four surgeons from the United States (Peggy Kelly MD, Douglas Sidell MD, Varun Vendra MD, Peter Koltai MD) and three from Zimbabwe (Clemence Chidziva MD, Naboth Matinhira MD, Titus Dzongodza MD).
Esophageal atresia (EA) is often associated with congenital heart disease (CHD). Repair of EA by the thoracoscopic approach places physiological stress on a newborn with CHD. This paper reviews the outcomes of infants with CHD who had undergone thoracoscopic EA repair, comparing their outcomes to those without CHD.
We present recent studies about newly developed or adjusted tools, the applicability of nutritional screening tools in specific populations, and how to implement screening in the overall process of improving nutritional care in the pediatric hospital setting. Summary Three new screening tools have been developed for use on admission to hospital: two for the mixed pediatric hospitalized population and one for infants. A simple weekly rescreening tool to identify hospital-acquired nutritional deterioration was developed for use in children with prolonged hospital stay. Different from most previous studies that only assess...
Until the successful repair of esophageal atresia (EA) and distal tracheoesophageal fistula (TEF) in 1941 by Cameron Haight of Ann Arbor, MI, every infant operated upon for this anomaly died within days and often hours of surgery. A key step was the posterior extrapleural approach to the mediastinum pioneered by Charles Mixter of Boston in 1929 that gave direct exposure of the anomaly without entering the pleural cavity and collapsing the lung. From 1936 to 1939 Thomas Lanman, also of Boston, made five unsuccessful attempts at primary repair of EA.
The purpose of this study was to investigate the effectiveness and safety of the operation for type III esophageal atresia using a thoracoscope.
Karuna M Das, Taleb M Almansoori, Tarek Suliman Momenah, Klaus Neidl-Van GorkomIndian Journal of Radiology and Imaging 2020 30(1):77-80 A patient of tetrology of Fallot with complete atresia of the pulmonary outflow tract with ventriculocoronary connections is presented.MDCT imaging revealed left coronary sinus, with a large fistula draining into the free wall of hypoplastic right ventricular cavity with tortuous channel arising from right ventricular outflow, and communicating with proximal limb of the fistula forming a complete loop suggesting a right ventricle–to – left coronary sinus sinusoid.
Distal vaginal atresia is a rare but psychosocially difficult congenital malformation that is often not recognized until a young patient presents with primary amenorrhea and typically concurrent abdominal pain. Vaginal atresia, or the failure of the vaginal plate to canalize, occurs secondary to failure of the urogenital sinus to form the lower portion of the vagina. The definitive management of distal vaginal atresia involves surgical drainage of the hematocolpos followed by anastomosis of the vaginal mucosa with the perineum.
Mayer-rokitansky-kuster-hauser (MRKH) syndrome is a congenital condition affecting 1 in 5000 females that results in vaginal agenesis. Mullerian anomalies such as those found in MRKH are also associated with MURCS (M üllerian duct aplasia–renal agenesis–cervicothoracic somite dysplasia) which is phenotypically similar to VACTERL (vertebral defects, anal atresia, cardiac defects, TE fistula, renal dysplasia, limb anomalies). All three of these conditions are believed to be multifactorial in nature, with pati ents having a typical chromosome complement.
We describe the imaging features of this entity and its demographics, imaging characteristics, treatment and prognosis.
Newborn screening for biliary atresia using direct or conjugated bilirubin measurements has a high diagnostic yield, detecting all known infants with the rare liver disorder in a large cross-sectional study of infants born at 14 Texas hospitals.Reuters Health Information
Objectives: Biliary atresia (BA) is the most common reason for liver transplant in childhood, and outcomes worsen with older age at hepatoportoenterostomy (HPE). We determined direct health care costs in children with BA, compared to controls in a population-based cohort of children in Ontario, Canada. Methods: We used health administrative data to identify all children diagnosed with BA between 2002 and 2016 (n = 121) and matched controls (n = 602). We determined annual direct healthcare costs, and rates of health services utilization, liver transplantation, death, portal hypertension, cirrhosis, esophageal v...