Management of giant embryonic vein in Klippel-Trénaunay syndrome

Publication date: July 2018Source: Journal of Vascular Surgery: Venous and Lymphatic Disorders, Volume 6, Issue 4Author(s): Animesh Rathore, Peter Gloviczki, Haraldur BjarnasonAbstractKlippel-Trénaunay syndrome is a rare mixed malformation characterized by congenital varicose veins, low-flow venous and lymphatic malformations, hypertrophy of soft tissue and bone, and capillary malformations. A 35-year-old man with a diagnosis of Klippel-Trénaunay syndrome presented to the clinic with significant pain and swelling in the left leg. Initial conservative management with compression therapy failed. He was then managed surgically with preoperative placement of an inferior vena cava filter (because of a history of deep venous thrombosis and pulmonary embolism), followed by resection of the lateral embryonic vein, ligation of large perforators, and excision of smaller varicosities. He is doing well at 18 months of follow-up.
Source: Journal of Vascular Surgery: Venous and Lymphatic Disorders - Category: Surgery Source Type: research