Severe Sprengel deformity associated with Klippel–Feil syndrome and a complex vascular abnormality that determined the corrective surgery technique

We present the case of an 11-year-old girl with severe SD and KFS. The left vertebral artery arose from the subclavian artery in a very high cervical location, which made surgical descent of the scapula unfeasible. The patient was treated using a Mears procedure, with osteotomy of the scapula and tenotomy of the long head of the triceps. The appearance and range of motion of the shoulders improved considerably, and there were no vascular complications. A morphologic vascular assessment is essential in children with SD and concomitant KFS to avoid potentially serious iatrogenic vascular injury when performing a scapular-descending surgical technique.
Source: Journal of Pediatric Orthopaedics B - Category: Orthopaedics Tags: Miscellaneous Source Type: research