An unusual case of pregnancy in a patient with Caroli ’s syndrome

Caroli ´s syndrome is a rare congenital disease with an incidence of 1:1,000,000 characterized by a non-obstructive segmental cystic dilation of large intrahepatic bile ducts [1]. There are two distinguishable forms: Caroli’s syndrome, which is associated with congenital hepatic fibrosis and cirrhosis a nd Caroli’s disease, a much more rare condition which is linked with autosomal recessive polycystic kidney disease [2]. Caroli’s syndrome can affect young women in their childbearing age, however, due its rare incidence there is paucity of data in the literature [2–4].

Source: European Journal of Obstetrics, Gynecology, and Reproductive Biology - June 15, 2018 Category: OBGYN Authors: Gabriel Levin, Lina Sabag, Alla Abu Khatab, Amihai Rottenstreich Tags: Correspondence Source Type: research