Ion Channel Dysfunctions in Dilated Cardiomyopathy in Limb-Girdle Muscular Dystrophy [Original Articles]
Conclusions:
This study demonstrates that patient-specific hiPSC cardiomyocytes can recapitulate some phenotypic properties of LGMD2I with DCM and provide a platform for studies on the cardiac events in LGMD.
Source: Circulation: Cardiovascular Genetics - Category: Cardiology Authors: El-Battrawy, I., Zhao, Z., Lan, H., Li, X., Yucel, G., Lang, S., Sattler, K., Schunemann, J.-D., Zimmermann, W.-H., Cyganek, L., Utikal, J., Wieland, T., Bieback, K., Bauer, R., Ratte, A., Pribe-Wolferts, R., Rapti, K., Nowak, D., Wittig, J., Thomas, D., Tags: Arrhythmias, Sudden Cardiac Death, Stem Cells, Translational Studies, Cardiomyopathy Original Articles Source Type: research
More News: Arrhythmia | Calcium | Cardiology | Cardiomyopathy | Cardiovascular | Dermatology | Dilated Cardiomyopathy | Genetics | Heart | Muscular Dystrophy | Potassium | Reflex Sympathetic Dystrophy | Stem Cell Therapy | Stem Cells | Study | Ventricular Tachycardia