Rupture of an abdominal aortic aneurysm in a young man with Marfan Syndrome

We present a case with a young non-smoking and normotensive male with Marfan syndrome, who developed an infrarenal abdominal aortic aneurysm that presented with rupture to the retroperitoneal cavity causing life-threatening bleeding shock. The patient had acute aortic surgery and survived. Five months before this incident, the patient had uneventful elective aortic root replacement (a.m David) due to an enlarged aortic root. At that time, his abdominal aorta was assessed with a routine ultrasound scan that showed a normal sized abdominal aorta.

Source: Annals of Vascular Surgery - February 5, 2018 Category: Surgery Authors: Maria Weinkouff Pedersen, Khiem Dinh Huynh, Ulrik Thorngren Baandrup, Dorte Guldbrand Nielsen, Niels Holmark Andersen Source Type: research