Screening for CRC cost effective in patients with cystic fibrosis
Natalia Molchanova, Hengzhuang Wang, Paul R. Hansen, Niels H øiby, Hanne M. Nielsen, Henrik Franzyk
THE parents of a little girl with cystic fibrosis have revealed their daily battle to keep her healthy as they wait for life-saving drug Orkambi
This study identifies educational needs and preferences of interprofessional CF providers regarding SRH in AYA women with CF.
We have read with great interest the case report by Pujol et al entitled Synchronous multiple non-small cell lung cancers in an allograft lung recipient , about a young cystic fibrosis lung transplant recipient who developed metastatic lung cancer. We would like to comment on this ‘rare’ long-term complication post lung transplantation. Recent registry data from the International Society of Heart and Lung Transplantation showed that the overall incidence of a malignancy post lung transplantation at 1, 5 and 10 years is 5.3%, 19.6% and 31.7% respectively  In observation al studies the incidence of lung can...
Conditions: Cystic Fibrosis; Hypoxemia; Lung Diseases Intervention: Other: Pre-flight evaluation Sponsors: Oslo University Hospital; The Norwegian Resouce Centre for Cystic Fibrosis; Norwegian National Adivisory Unit on Rare Disorders; LHL Hospital Gardermoen Not yet recruiting
Publication date: Available online 16 February 2019Source: Journal de Mycologie MédicaleAuthor(s): M. Hassanzad, V. Mortezaee, F. Bongomin, M. Poorabdollah, S. Sharifynia, M. Maleki, N. Hedayati, A.A. Velayati, M.T. HedayatiAbstractA 12-year-old boy with cystic fibrosis (CF) and a history of glucocorticoid-dependent allergic bronchopulmonary aspergillosis (ABPA) was referred to our hospital. The ABPA was diagnosed when he was 8 years old and he had been treated with several course of oral glucocorticoids for recurrent exacerbations. He was readmitted when aged 12 with a history of worsening shortness of breath and c...
We present our experience with distal splenorenal shunting (DSRS) for the treatment of PHT as an alternative to liver transplantation (LT).
In response, we thank Professor Millar and Ms. Bell for their interest in our article . Our group and others have published on the ease of use and effectiveness of thermal based disinfection methods [2 –4]. We agree that additional studies are required before a final determination is made regarding the routine use of thermal disinfection. We are currently engaged in further examination of varied disinfection techniques and nebulizers to identify the most effective method that is user-friendly an d preserves optimal nebulizer function prior to making any definitive recommendations to the CF community.
We report the initiation of CFTR modulator lumacaftor/ivacaftor combination (LUM/IVA) in two adolescents with cystic fibrosis who were treated with antifungal azoles (AZO) and tacrolimus (TCS) for liver transplantation. Despite multiple drug ‐drug interactions, maintaining therapeutic TCS levels was achievable. During the following year, LUM/IVA was well tolerated, providing clinical benefits. Key Clinical MessageWe report the initiation of CFTR modulator lumacaftor/ivacaftor combination (LUM/IVA) in two adolescents with cystic fibrosis who were treated with antifungal azoles (AZO) and tacrolimus (TCS) for liver transpla...