Single-Ventricle Palliation in a 4-Year-Old With Ehlers-Danlos Syndrome.

We report the case of a 4-year-old boy with Ehlers-Danlos syndrome undergoing single-ventricle palliation for an unbalanced atrioventricular canal defect. No reports of single-ventricle palliation in the setting of connective tissue disorders exist in the current literature. Unique findings on the patient's preoperative imaging included a disproportionately large neoaortic root and a regurgitant atrioventricular valve, which may foretell the need for future intervention. PMID: 29233360 [PubMed - in process]

https://www.ncbi.nlm.nih.gov/pubmed/29233360?dopt=Abstract

Source: The Annals of Thoracic Surgery - December 15, 2017 Category: Cardiovascular & Thoracic Surgery Authors: DeBoard ZM, Eckhauser AW, Griffiths E Tags: Ann Thorac Surg Source Type: research

More News: Cardiovascular & Thoracic Surgery | Ehlers-Danlos Syndrome