A histopathological connection between a fatal endolymphatic sac tumour and von Hippel-Lindau disease from 1960.

CONCLUSION: Endolymphatic sac tumours are rare neoplasms of the temporal bone that can occur sporadically or as part of von Hippel-Lindau disease. The connection between endolymphatic sac tumour and von Hippel-Lindau disease was first proposed in 1988 and formalised in 1997. We believe that this case represents the first documented connection between endolymphatic sac tumour and von Hippel-Lindau disease.
PMID: 28874214 [PubMed - as supplied by publisher]

Source: Journal of Laryngology and Otology - September 8, 2017 Category: ENT & OMF Tags: J Laryngol Otol Source Type: research