A biventricular repair for Jayce ’s one-of-a-kind heart

Amanda Mattioli was working in Afghanistan as a government contractor and had just completed a whirlwind round of travel to three separate continents when she learned she was pregnant. The helicopter unit that took her back to the main base so she could return home for her pregnancy gave her a unit sticker to commemorate her baby’s first helicopter ride. Little did she know it would also mark the beginning of a much longer journey for her and her son, William “Jayce” James. Amanda got her first hint the ride would be bumpy at her 20-week ultrasound, when she learned Jayce’s heart was on the right side of his chest, rather than the left side. She was sent to a hospital in nearby Pittsburgh for a level 2 ultrasound, where doctors discovered Jayce had three other major heart defects: complete atrioventricular canal defect (AV canal), transposition of the great arteries (TGA) and pulmonary atresia. Amanda was also referred to a geneticist. The geneticist told her it was very likely he had trisomy 18, a genetic disorder that causes severe birth defects. “She said he probably wouldn’t make it to birth, and if he did, he wouldn’t make it more than a few hours.” Amanda, overwhelmed and upset by the way this news had been delivered, returned to her local doctor and was referred to a private cardiologist in Pittsburgh for a second opinion, Dr. Prapti Kanani, a former cardiology fellow at Boston Children’s Hospital. Finding a b...
Source: Thrive, Children's Hospital Boston - Category: Pediatrics Authors: Tags: Diseases & Conditions Our Patients’ Stories atrioventricular canal Biventricular Repair Biventricular Repair Program Dr. Gerald Marx Dr. Pedro del Nido Heterotaxy syndrome Pulmonary atresia transposition of the great arteries Source Type: news

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Publication date: Available online 14 January 2019Source: Case Reports in Women's HealthAuthor(s): Danielle Robson, Vanessa Lusink, Neil CampbellAbstract2% of all pregnancies are ectopic. Optimal surgical management is currently salpingectomy over salpingostomy, secondary to the risks of persistent trophoblastic tissue or omental implants (15%). However, rare cases of omental trophoblastic implants following laparoscopic salpingectomy have been noted in the literature. Current practice dictates that serial determinations of human chorionic gonadotropin (beta-hCG) levels after salpingectomy are not required, as it is consid...
Source: Case Reports in Womens Health - Category: OBGYN Source Type: research
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Source: Acta Paulista de Enfermagem - Category: Nursing Source Type: research
ConclusionsDoppler ultrasound in our neurosonology laboratory was found to be a useful diagnostic tool for detecting cervical carotid artery stenosis and demonstrated superiority to carotid duplex despite the lack of B-mode. Furthermore, this technique was found to be useful for detecting intracranial stenosis.ResumenIntroducciónLa detección de estenosis arterial cervical e intracraneal es fundamental en el estudio del ictus isquémico, al ser el origen aterotrombótico el más prevalente en nuestro entorno. La ultrasonografía se ha convertido, por su accesibilidad y fiabilidad, en la...
Source: Neurologia - Category: Neurology Source Type: research
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Source: Cerebrovascular Diseases - Category: Neurology Source Type: research
Edwards Lifesciences is resolving its longstanding dispute with Boston Scientific over transcatheter aortic valve replacement (TAVR) patents. However, this time the Irvine, CA-based company is on the other side of the lawsuit coin and is poised to dole out a one-time payment of $180 million to Boston Scientific. Both companies said that no further royalty fees will be owed by any company. In addition, both companies said that all pending cases or appeals in courts and patent offices will be dismissed, and the parties will not litigate patent disputes related to current portfolios of transcatheter aortic valves, certain mit...
Source: MDDI - Category: Medical Devices Authors: Tags: Business Cardiovascular Source Type: news
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Source: Journal of Hepatology - Category: Gastroenterology Authors: Tags: Review Source Type: research
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Source: Journal of Hepatology - Category: Gastroenterology Authors: Tags: Review Source Type: research
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Source: Journal of Critical Care - Category: Gastroenterology Source Type: research
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Source: Journal of Pharmaceutical and Biomedical Analysis - Category: Drugs & Pharmacology Source Type: research
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